NorUDCA promotes degradation of α1-antitrypsin mutant Z protein by inducing autophagy through AMPK/ULK1 pathway

por Tang, Youcai, Blomenkamp, Keith S., Fickert, Peter, Trauner, Michael, Teckman, Jeffrey H.
Publicado 2018

Knockdown of Alpha-1 Antitrypsin with antisense oligonucleotide does not exacerbate smoke induced lung injury

por Stearns, Kyle, Goldklang, Monica, Xiao, Rui, Zelonina, Tina, Blomenkamp, Keith, Teckman, Jeffery, D’Armiento, Jeanine M.
Publicado 2021

PiZ Mouse Liver Accumulates Polyubiquitin Conjugates That Associate with Catalytically Active 26S Proteasomes

por Haddock, Christopher J., Blomenkamp, Keith, Gautam, Madhav, James, Jared, Mielcarska, Joanna, Gogol, Edward, Teckman, Jeffrey, Skowyra, Dorota
Publicado 2014

Sustained miRNA-mediated Knockdown of Mutant AAT With Simultaneous Augmentation of Wild-type AAT Has Minimal Effect on Global Liver miRNA Profiles

por Mueller, Christian, Tang, Qiushi, Gruntman, Alisha, Blomenkamp, Keith, Teckman, Jeffery, Song, Lina, Zamore, Phillip D, Flotte, Terence R
Publicado 2012

Role of the Gut–Liver Axis in Driving Parenteral Nutrition-Associated Injury

por Denton, Christine, Price, Amber, Friend, Julie, Manithody, Chandrashekhara, Blomenkamp, Keith, Westrich, Matthew, Kakarla, Vindhya, Phillips, William, Krebs, Joseph, Munoz Abraham, Armando Salim, Osei, Hector, Jain, Ajay Kumar
Publicado 2018

Gene transfer of master autophagy regulator TFEB results in clearance of toxic protein and correction of hepatic disease in alpha-1-anti-trypsin deficiency

por Pastore, Nunzia, Blomenkamp, Keith, Annunziata, Fabio, Piccolo, Pasquale, Mithbaokar, Pratibha, Maria Sepe, Rosa, Vetrini, Francesco, Palmer, Donna, Ng, Philip, Polishchuk, Elena, Iacobacci, Simona, Polishchuk, Roman, Teckman, Jeffrey, Ballabio, Andrea, Brunetti-Pierri, Nicola
Publicado 2013