Levels of α7 integrin and laminin-α2 are increased following prednisone treatment in the mdx mouse and GRMD dog models of Duchenne muscular dystrophy

por Wuebbles, Ryan D., Sarathy, Apurva, Kornegay, Joe N., Burkin, Dean J.
Publicado 2013

Vemurafenib improves muscle histopathology in a mouse model of LAMA2-related congenital muscular dystrophy

por Oliveira-Santos, Ariany, Dagda, Marisela, Wittmann, Jennifer, Smalley, Robert, Burkin, Dean J.
Publicado 2023

Laminin and Integrin in LAMA2-Related Congenital Muscular Dystrophy: From Disease to Therapeutics

por Barraza-Flores, Pamela, Bates, Christina R., Oliveira-Santos, Ariany, Burkin, Dean J.
Publicado 2020

A Functional Role for Specific Spliced Variants of the α7β1 Integrin in Acetylcholine Receptor Clustering

por Burkin, Dean J., Gu, Maojian, Hodges, Bradley L., Campanelli, James T., Kaufman, Stephen J.
Publicado 1998

Commentary: SU9516 increases α7β1 Integrin and Ameliorates Disease Progression in the mdx Mouse Model of Duchenne Muscular Dystrophy

por Sarathy, Apurva, Nunes, Andreia M., Fontelonga, Tatiana M., Ogata, Tracy Y., Burkin, Dean J.
Publicado 2017

Enhanced Expression of the α7β1 Integrin Reduces Muscular Dystrophy and Restores Viability in Dystrophic Mice

por Burkin, Dean J., Wallace, Gregory Q., Nicol, Kimberly J., Kaufman, David J., Kaufman, Stephen J.
Publicado 2001

Human laminin-111 and laminin-211 protein therapy prevents muscle disease progression in an immunodeficient mouse model of LAMA2-CMD

por Barraza-Flores, Pamela, Hermann, Hailey J., Bates, Christina R., Allen, Tyler G., Grunert, Timothy T., Burkin, Dean J.
Publicado 2020

Human Galectin-1 Improves Sarcolemma Stability and Muscle Vascularization in the mdx Mouse Model of Duchenne Muscular Dystrophy

por Wuebbles, Ryan D., Cruz, Vivian, Van Ry, Pam, Barraza-Flores, Pamela, Brewer, Paul D., Jones, Peter, Burkin, Dean J.
Publicado 2019

Transgenic overexpression of α7 integrin in smooth muscle attenuates allergen‐induced airway inflammation in a murine model of asthma

por Ba, Mariam A., Aiyuk, Annemarie, Hernández, Karla, Evasovic, Jon M., Wuebbles, Ryan D., Burkin, Dean J., Singer, Cherie A.
Publicado 2022

NMRK2 Gene Is Upregulated in Dilated Cardiomyopathy and Required for Cardiac Function and NAD Levels during Aging

por Tannous, Cynthia, Deloux, Robin, Karoui, Ahmed, Mougenot, Nathalie, Burkin, Dean, Blanc, Jocelyne, Coletti, Dario, Lavery, Gareth, Li, Zhenlin, Mericskay, Mathias
Publicado 2021

Transgenic mice expressing tunable levels of DUX4 develop characteristic facioscapulohumeral muscular dystrophy-like pathophysiology ranging in severity

por Jones, Takako I., Chew, Guo-Liang, Barraza-Flores, Pamela, Schreier, Spencer, Ramirez, Monique, Wuebbles, Ryan D., Burkin, Dean J., Bradley, Robert K., Jones, Peter L.
Publicado 2020

Improving Reproducibility of Phenotypic Assessments in the DyW Mouse Model of Laminin-α2 Related Congenital Muscular Dystrophy

por Willmann, Raffaella, Gordish-Dressman, Heather, Meinen, Sarina, Rüegg, Markus A., Yu, Qing, Nagaraju, Kanneboyina, Kumar, Ayar, Girgenrath, Mahasweta, Coffey, Caroline B.M., Cruz, Vivian, Van Ry, Pam M., Bogdanik, Laurent, Lutz, Cathleen, Rutkowski, Anne, Burkin, Dean J.
Publicado 2017

Integrin α7 Mutations Are Associated With Adult‐Onset Cardiac Dysfunction in Humans and Mice

por Bugiardini, Enrico, Nunes, Andreia M., Oliveira‐Santos, Ariany, Dagda, Marisela, Fontelonga, Tatiana M., Barraza‐Flores, Pamela, Pittman, Alan M., Morrow, Jasper M., Parton, Matthew, Houlden, Henry, Elliott, Perry M., Syrris, Petros, Maas, Roderick P., Akhtar, Mohammed M., Küsters, Benno, Raaphorst, Joost, Schouten, Meyke, Kamsteeg, Erik‐Jan, van Engelen, Baziel, Hanna, Michael G., Phadke, Rahul, Lopes, Luis R., Matthews, Emma, Burkin, Dean J.
Publicado 2022