An atypical Ca(V)1.1 mutation reveals a common mechanism for hypokalemic periodic paralysis

por Cannon, Stephen C.
Publicado 2017

A role for external Ca(2+) in maintaining muscle contractility in periodic paralysis

por Cannon, Stephen C.
Publicado 2020

Slow Inactivation Does Not Affect Movement of the Fast Inactivation Gate in Voltage-gated Na(+) Channels

por Vedantham, Vasanth, Cannon, Stephen C.
Publicado 1998

The Position of the Fast-Inactivation Gate during Lidocaine Block of Voltage-gated Na(+) Channels

por Vedantham, Vasanth, Cannon, Stephen C.
Publicado 1999

A Na(+) Channel Mutation Linked to Hypokalemic Periodic Paralysis Exposes a Proton-selective Gating Pore

por Struyk, Arie F., Cannon, Stephen C.
Publicado 2007

Slow Inactivation Does Not Block the Aqueous Accessibility to the Outer Pore of Voltage-gated Na Channels

por Struyk, Arie F., Cannon, Stephen C.
Publicado 2002

Cooh-Terminal Truncated Alpha(1S) Subunits Conduct Current Better than Full-Length Dihydropyridine Receptors

por Morrill, James A., Cannon, Stephen C.
Publicado 2000

Disrupted coupling of gating charge displacement to Na(+) current activation for DIIS4 mutations in hypokalemic periodic paralysis

por Mi, Wentao, Rybalchenko, Volodymyr, Cannon, Stephen C.
Publicado 2014

Gating pore currents occur in Ca(V)1.1 domain III mutants associated with HypoPP

por Wu, Fenfen, Quinonez, Marbella, Cannon, Stephen C.
Publicado 2021

A four-electrode method to study dynamics of ion activity and transport in skeletal muscle fibers

por Heiny, Judith A., Cannon, Stephen C., DiFranco, Marino
Publicado 2019

Retigabine suppresses loss of force in mouse models of hypokalaemic periodic paralysis

por Quiñonez, Marbella, DiFranco, Marino, Wu, Fenfen, Cannon, Stephen C
Publicado 2023

Gating Pore Currents in DIIS4 Mutations of NaV1.4 Associated with Periodic Paralysis: Saturation of Ion Flux and Implications for Disease Pathogenesis

por Struyk, Arie F., Markin, Vladislav S., Francis, David, Cannon, Stephen C.
Publicado 2008

Stac3 enhances expression of human Ca(V)1.1 in Xenopus oocytes and reveals gating pore currents in HypoPP mutant channels

por Wu, Fenfen, Quinonez, Marbella, DiFranco, Marino, Cannon, Stephen C.
Publicado 2018

Recovery from acidosis is a robust trigger for loss of force in murine hypokalemic periodic paralysis

por Mi, Wentao, Wu, Fenfen, Quinonez, Marbella, DiFranco, Marino, Cannon, Stephen C.
Publicado 2019

A highly-selective chloride microelectrode based on a mercuracarborand anion carrier

por DiFranco, Marino, Quinonez, Marbella, Dziedzic, Rafal M., Spokoyny, Alexander M., Cannon, Stephen C.
Publicado 2019

Resurgent and Gating Pore Currents Induced by De Novo SCN2A Epilepsy Mutations

por Mason, Emily R., Wu, Fenfen, Patel, Reesha R., Xiao, Yucheng, Cannon, Stephen C., Cummins, Theodore R.
Publicado 2019

Myotonic Myopathy With Secondary Joint and Skeletal Anomalies From the c.2386C>G, p.L796V Mutation in SCN4A

por Elia, Nathaniel, Nault, Trystan, McMillan, Hugh J., Graham, Gail E., Huang, Lijia, Cannon, Stephen C.
Publicado 2020

Corrigendum: Myotonic Myopathy With Secondary Joint and Skeletal Anomalies From the c.2386C>G, p.L796V Mutation in SCN4A

por Elia, Nathaniel, Nault, Trystan, McMillan, Hugh J., Graham, Gail E., Huang, Lijia, Cannon, Stephen C.
Publicado 2020

The distinct role of the four voltage sensors of the skeletal Ca(V)1.1 channel in voltage-dependent activation

por Savalli, Nicoletta, Angelini, Marina, Steccanella, Federica, Wier, Julian, Wu, Fenfen, Quinonez, Marbella, DiFranco, Marino, Neely, Alan, Cannon, Stephen C., Olcese, Riccardo
Publicado 2021

Myasthenic congenital myopathy from recessive mutations at a single residue in Na(V)1.4

por Elia, Nathaniel, Palmio, Johanna, Castañeda, Marisol Sampedro, Shieh, Perry B., Quinonez, Marbella, Suominen, Tiina, Hanna, Michael G., Männikkö, Roope, Udd, Bjarne, Cannon, Stephen C.
Publicado 2019