Advancement in Nanostructure-Based Tissue-Engineered Biomaterials for Retinal Degenerative Diseases

por Rohiwal, Sonali Suresh, Ellederová, Zdenka, Ardan, Taras, Klima, Jiri
Publicado 2021

Longitudinal study revealing motor, cognitive and behavioral decline in a transgenic minipig model of Huntington's disease

por Baxa, Monika, Levinska, Bozena, Skrivankova, Monika, Pokorny, Matous, Juhasova, Jana, Klima, Jiri, Klempir, Jiri, Motlík, Jan, Juhas, Stefan, Ellederova, Zdenka
Publicado 2019

Large Animal Models of Huntington’s Disease: What We Have Learned and Where We Need to Go Next

por Howland, David, Ellederova, Zdenka, Aronin, Neil, Fernau, Deborah, Gallagher, Jill, Taylor, Amanda, Hennebold, Jon, Weiss, Alison R., Gray-Edwards, Heather, McBride, Jodi
Publicado 2020

Transgenic minipig model of Huntington's disease exhibiting gradually progressing neurodegeneration

por Ardan, Taras, Baxa, Monika, Levinská, Božena, Sedláčková, Miroslava, Nguyen, The Duong, Klíma, Jiří, Juhás, Štefan, Juhásová, Jana, Šmatlíková, Petra, Vochozková, Petra, Motlík, Jan, Ellederová, Zdenka
Publicado 2019

Cks Overexpression Enhances Chemotherapeutic Efficacy by Overriding DNA Damage Checkpoints

por del Rincón, Sonia V., Widschwendter, Martin, Sun, Dahui, Ekholm-Reed, Susanna, Tat, John, Teixeira, Leonardo K., Ellederova, Zdenka, Grolieres, Elise, Reed, Steven I., Spruck, Charles
Publicado 2014

Deterioration of mitochondrial bioenergetics and ultrastructure impairment in skeletal muscle of a transgenic minipig model in the early stages of Huntington's disease

por Rodinova, Marie, Krizova, Jana, Stufkova, Hana, Bohuslavova, Bozena, Askeland, Georgina, Dosoudilova, Zaneta, Juhas, Stefan, Juhasova, Jana, Ellederova, Zdenka, Zeman, Jiri, Eide, Lars, Motlik, Jan, Hansikova, Hana
Publicado 2019

A transgenic minipig model of Huntington's disease shows early signs of behavioral and molecular pathologies

por Askeland, Georgina, Rodinova, Marie, Štufková, Hana, Dosoudilova, Zaneta, Baxa, Monika, Smatlikova, Petra, Bohuslavova, Bozena, Klempir, Jiri, Nguyen, The Duong, Kuśnierczyk, Anna, Bjørås, Magnar, Klungland, Arne, Hansikova, Hana, Ellederova, Zdenka, Eide, Lars
Publicado 2018

Development of an AAV-Based MicroRNA Gene Therapy to Treat Machado-Joseph Disease

por Martier, Raygene, Sogorb-Gonzalez, Marina, Stricker-Shaver, Janice, Hübener-Schmid, Jeannette, Keskin, Sonay, Klima, Jiri, Toonen, Lodewijk J., Juhas, Stefan, Juhasova, Jana, Ellederova, Zdenka, Motlik, Jan, Haas, Eva, van Deventer, Sander, Konstantinova, Pavlina, Nguyen, Huu Phuc, Evers, Melvin M.
Publicado 2019

AAV5-miHTT Gene Therapy Demonstrates Broad Distribution and Strong Human Mutant Huntingtin Lowering in a Huntington’s Disease Minipig Model

por Evers, Melvin M., Miniarikova, Jana, Juhas, Stefan, Vallès, Astrid, Bohuslavova, Bozena, Juhasova, Jana, Skalnikova, Helena Kupcova, Vodicka, Petr, Valekova, Ivona, Brouwers, Cynthia, Blits, Bas, Lubelski, Jacek, Kovarova, Hana, Ellederova, Zdenka, van Deventer, Sander J., Petry, Harald, Motlik, Jan, Konstantinova, Pavlina
Publicado 2018

Subretinal Implantation of Human Primary RPE Cells Cultured on Nanofibrous Membranes in Minipigs

por Lytvynchuk, Lyubomyr, Ebbert, Annabelle, Studenovska, Hana, Nagymihály, Richárd, Josifovska, Natasha, Rais, David, Popelka, Štěpán, Tichotová, Lucie, Nemesh, Yaroslav, Čížková, Jana, Juhásová, Jana, Juhás, Štefan, Jendelová, Pavla, Franeková, Janka, Kozak, Igor, Erceg, Slaven, Straňák, Zbynek, Müller, Brigitte, Ellederová, Zdenka, Motlík, Jan, Stieger, Knut, Ardan, Taras, Petrovski, Goran
Publicado 2022

Early disruption of photoreceptor cell architecture and loss of vision in a humanized pig model of usher syndromes

por Grotz, Sophia, Schäfer, Jessica, Wunderlich, Kirsten A, Ellederova, Zdenka, Auch, Hannah, Bähr, Andrea, Runa‐Vochozkova, Petra, Fadl, Janet, Arnold, Vanessa, Ardan, Taras, Veith, Miroslav, Santamaria, Gianluca, Dhom, Georg, Hitzl, Wolfgang, Kessler, Barbara, Eckardt, Christian, Klein, Joshua, Brymova, Anna, Linnert, Joshua, Kurome, Mayuko, Zakharchenko, Valeri, Fischer, Andrea, Blutke, Andreas, Döring, Anna, Suchankova, Stepanka, Popelar, Jiri, Rodríguez‐Bocanegra, Eduardo, Dlugaiczyk, Julia, Straka, Hans, May‐Simera, Helen, Wang, Weiwei, Laugwitz, Karl‐Ludwig, Vandenberghe, Luk H, Wolf, Eckhard, Nagel‐Wolfrum, Kerstin, Peters, Tobias, Motlik, Jan, Fischer, M Dominik, Wolfrum, Uwe, Klymiuk, Nikolai
Publicado 2022