The ΔF508-CFTR mutation inhibits wild-type CFTR processing and function when co-expressed in human airway epithelia and in mouse nasal mucosa

por Tucker, Torry A, Fortenberry, James A, Zsembery, Akos, Schwiebert, Lisa M, Schwiebert, Erik M
Publicado 2012

Characterization of Defects in Ion Transport and Tissue Development in Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)-Knockout Rats

por Tuggle, Katherine L., Birket, Susan E., Cui, Xiaoxia, Hong, Jeong, Warren, Joe, Reid, Lara, Chambers, Andre, Ji, Diana, Gamber, Kevin, Chu, Kengyeh K., Tearney, Guillermo, Tang, Li Ping, Fortenberry, James A., Du, Ming, Cadillac, Joan M., Bedwell, David M., Rowe, Steven M., Sorscher, Eric J., Fanucchi, Michelle V.
Publicado 2014