Iron Deficiency without Anemia Decreases Physical Endurance and Mitochondrial Complex I Activity of Oxidative Skeletal Muscle in the Mouse

por Rineau, Emmanuel, Gueguen, Naïg, Procaccio, Vincent, Geneviève, Franck, Reynier, Pascal, Henrion, Daniel, Lasocki, Sigismond
Publicado 2021

Overexpression of the Mitochondrial T3 Receptor p43 Induces a Shift in Skeletal Muscle Fiber Types

por Casas, François, Pessemesse, Laurence, Grandemange, Stéphanie, Seyer, Pascal, Gueguen, Naïg, Baris, Olivier, Lepourry, Laurence, Cabello, Gérard, Wrutniak-Cabello, Chantal
Publicado 2008

Estrogen-Related Receptor Alpha Modulates Lactate Dehydrogenase Activity in Thyroid Tumors

por Mirebeau-Prunier, Delphine, Le Pennec, Soazig, Jacques, Caroline, Fontaine, Jean-Fred, Gueguen, Naig, Boutet-Bouzamondo, Nathalie, Donnart, Audrey, Malthièry, Yves, Savagner, Frédérique
Publicado 2013

Overexpression of the Mitochondrial T3 Receptor Induces Skeletal Muscle Atrophy during Aging

por Casas, François, Pessemesse, Laurence, Grandemange, Stéphanie, Seyer, Pascal, Baris, Olivier, Gueguen, Naïg, Ramonatxo, Christelle, Perrin, Florence, Fouret, Gilles, Lepourry, Laurence, Cabello, Gérard, Wrutniak-Cabello, Chantal
Publicado 2009

Doxorubicin-Induced Autophagolysosome Formation Is Partly Prevented by Mitochondrial ROS Elimination in DOX-Resistant Breast Cancer Cells

por Ahmadpour, Seyedeh Tayebeh, Desquiret-Dumas, Valérie, Yikilmaz, Ulku, Dartier, Julie, Domingo, Isabelle, Wetterwald, Celine, Orre, Charlotte, Gueguen, Naïg, Brisson, Lucie, Mahéo, Karine, Dumas, Jean-François
Publicado 2021

Resveratrol Directly Binds to Mitochondrial Complex I and Increases Oxidative Stress in Brain Mitochondria of Aged Mice

por Gueguen, Naïg, Desquiret-Dumas, Valérie, Leman, Géraldine, Chupin, Stéphanie, Baron, Stéphanie, Nivet-Antoine, Valérie, Vessières, Emilie, Ayer, Audrey, Henrion, Daniel, Lenaers, Guy, Reynier, Pascal, Procaccio, Vincent
Publicado 2015

Case report: Thirty-year progression of an EMPF1 encephalopathy due to defective mitochondrial and peroxisomal fission caused by a novel de novo heterozygous DNM1L variant

por Lhuissier, Charlène, Wagner, Bart E., Vincent, Amy, Garraux, Gaëtan, Hougrand, Olivier, Van Coster, Rudy, Benoit, Valerie, Karadurmus, Deniz, Lenaers, Guy, Gueguen, Naïg, Chevrollier, Arnaud, Maystadt, Isabelle
Publicado 2022

Autophagy controls the pathogenicity of OPA1 mutations in dominant optic atrophy

por Kane, Mariame Selma, Alban, Jennifer, Desquiret‐Dumas, Valérie, Gueguen, Naïg, Ishak, Layal, Ferre, Marc, Amati‐Bonneau, Patrizia, Procaccio, Vincent, Bonneau, Dominique, Lenaers, Guy, Reynier, Pascal, Chevrollier, Arnaud
Publicado 2017

Novel NDUFS4 gene mutation in an atypical late-onset mitochondrial form of multifocal dystonia

por Bris, Celine, Rouaud, Tiphaine, Desquiret-Dumas, Valerie, Gueguen, Naig, Goudenege, David, Barth, Magalie, Bonneau, Dominique, Amati-Bonneau, Patrizia, Lenaers, Guy, Reynier, Pascal, Lebre, Anne-Sophie, Procaccio, Vincent
Publicado 2017

Acute and late-onset optic atrophy due to a novel OPA1 mutation leading to a mitochondrial coupling defect

por Nochez, Yannick, Arsene, Sophie, Gueguen, Naig, Chevrollier, Arnaud, Ferré, Marc, Guillet, Virginie, Desquiret, Valérie, Toutain, Annick, Bonneau, Dominique, Procaccio, Vincent, Amati-Bonneau, Patrizia, Pisella, Pierre-Jean, Reynier, Pascal
Publicado 2009

Idebenone increases mitochondrial complex I activity in fibroblasts from LHON patients while producing contradictory effects on respiration

por Angebault, Claire, Gueguen, Naïg, Desquiret-Dumas, Valérie, Chevrollier, Arnaud, Guillet, Virginie, Verny, Christophe, Cassereau, Julien, Ferre, Marc, Milea, Dan, Amati-Bonneau, Patrizia, Bonneau, Dominique, Procaccio, Vincent, Reynier, Pascal, Loiseau, Dominique
Publicado 2011

The Long Non-Coding RNA SAMMSON Is a Regulator of Chemosensitivity and Metabolic Orientation in MCF-7 Doxorubicin-Resistant Breast Cancer Cells

por Orre, Charlotte, Dieu, Xavier, Guillon, Jordan, Gueguen, Naïg, Ahmadpour, Seyedeh Tayebeh, Dumas, Jean-François, Khiati, Salim, Reynier, Pascal, Lenaers, Guy, Coqueret, Olivier, Chevrollier, Arnaud, Mirebeau-Prunier, Delphine, Desquiret-Dumas, Valérie
Publicado 2021

Acetoacetate protects macrophages from lactic acidosis-induced mitochondrial dysfunction by metabolic reprograming

por Adam, Clément, Paolini, Léa, Gueguen, Naïg, Mabilleau, Guillaume, Preisser, Laurence, Blanchard, Simon, Pignon, Pascale, Manero, Florence, Le Mao, Morgane, Morel, Alain, Reynier, Pascal, Beauvillain, Céline, Delneste, Yves, Procaccio, Vincent, Jeannin, Pascale
Publicado 2021

Kynurenic Acid: A Novel Player in Cardioprotection against Myocardial Ischemia/Reperfusion Injuries

por Kamel, Rima, Baetz, Delphine, Gueguen, Naïg, Lebeau, Lucie, Barbelivien, Agnès, Guihot, Anne-Laure, Allawa, Louwana, Gallet, Jean, Beaumont, Justine, Ovize, Michel, Henrion, Daniel, Reynier, Pascal, Mirebeau-Prunier, Delphine, Prunier, Fabrice, Tamareille, Sophie
Publicado 2023

Next-Generation Sequencing Identifies Novel PMPCA Variants in Patients with Late-Onset Dominant Optic Atrophy

por Charif, Majida, Chevrollier, Arnaud, Gueguen, Naïg, Kane, Selma, Bris, Céline, Goudenège, David, Desquiret-Dumas, Valerie, Meunier, Isabelle, Mochel, Fanny, Jeanjean, Luc, Varenne, Fanny, Procaccio, Vincent, Reynier, Pascal, Bonneau, Dominique, Amati-Bonneau, Patrizia, Lenaers, Guy
Publicado 2022

Increased Protein S-Glutathionylation in Leber’s Hereditary Optic Neuropathy (LHON)

por Zhou, Lei, Chan, James Chun Yip, Chupin, Stephanie, Gueguen, Naïg, Desquiret-Dumas, Valérie, Koh, Siew Kwan, Li, Jianguo, Gao, Yan, Deng, Lu, Verma, Chandra, Beuerman, Roger W, Chan, Eric Chun Yong, Milea, Dan, Reynier, Pascal
Publicado 2020

DRP1 haploinsufficiency attenuates cardiac ischemia/reperfusion injuries

por Bouche, Laura, Kamel, Rima, Tamareille, Sophie, Garcia, Gabriel, Villedieu, Camille, Pillot, Bruno, Gueguen, Naïg, Chehaitly, Ahmad, Chao de la Barca, Juan Manuel, Beaumont, Justine, Baetz, Delphine, Ovize, Michel, Sesaki, Hiromi, Henrion, Daniel, Reynier, Pascal, Lenaers, Guy, Prunier, Fabrice, Mirebeau-Prunier, Delphine
Publicado 2021

Glutamate-Induced Deregulation of Krebs Cycle in Mitochondrial Encephalopathy Lactic Acidosis Syndrome Stroke-Like Episodes (MELAS) Syndrome Is Alleviated by Ketone Body Exposure

por Belal, Sophie, Goudenège, David, Bocca, Cinzia, Dumont, Florent, Chao De La Barca, Juan Manuel, Desquiret-Dumas, Valérie, Gueguen, Naïg, Geffroy, Guillaume, Benyahia, Rayane, Kane, Selma, Khiati, Salim, Bris, Céline, Aranyi, Tamas, Stockholm, Daniel, Inisan, Aurore, Renaud, Aurélie, Barth, Magalie, Simard, Gilles, Reynier, Pascal, Letournel, Franck, Lenaers, Guy, Bonneau, Dominique, Chevrollier, Arnaud, Procaccio, Vincent
Publicado 2022

Mutations in the m-AAA proteases AFG3L2 and SPG7 are causing isolated dominant optic atrophy

por Charif, Majida, Chevrollier, Arnaud, Gueguen, Naïg, Bris, Céline, Goudenège, David, Desquiret-Dumas, Valérie, Leruez, Stéphanie, Colin, Estelle, Meunier, Audrey, Vignal, Catherine, Smirnov, Vasily, Defoort-Dhellemmes, Sabine, Drumare Bouvet, Isabelle, Goizet, Cyril, Votruba, Marcela, Jurkute, Neringa, Yu-Wai-Man, Patrick, Tagliavini, Francesca, Caporali, Leonardo, La Morgia, Chiara, Carelli, Valerio, Procaccio, Vincent, Zanlonghi, Xavier, Meunier, Isabelle, Reynier, Pascal, Bonneau, Dominique, Amati-Bonneau, Patrizia, Lenaers, Guy
Publicado 2020

Dominant ACO2 mutations are a frequent cause of isolated optic atrophy

por Charif, Majida, Gueguen, Naïg, Ferré, Marc, Elkarhat, Zouhair, Khiati, Salim, LeMao, Morgane, Chevrollier, Arnaud, Desquiret-Dumas, Valerie, Goudenège, David, Bris, Céline, Kane, Selma, Alban, Jennifer, Chupin, Stéphanie, Wetterwald, Céline, Caporali, Leonardo, Tagliavini, Francesca, LaMorgia, Chiara, Carbonelli, Michele, Jurkute, Neringa, Barakat, Abdelhamid, Gohier, Philippe, Verny, Christophe, Barth, Magalie, Procaccio, Vincent, Bonneau, Dominique, Zanlonghi, Xavier, Meunier, Isabelle, Weisschuh, Nicole, Schimpf-Linzenbold, Simone, Tonagel, Felix, Kellner, Ulrich, Yu-Wai-Man, Patrick, Carelli, Valerio, Wissinger, Bernd, Amati-Bonneau, Patrizia, Reynier, Pascal, Lenaers, Guy
Publicado 2021