Cell-autonomous axon growth of young motoneurons is triggered by a voltage-gated sodium channel

por Wetzel, Andrea, Jablonka, Sibylle, Blum, Robert
Publicado 2013

Differentiation defects in primary motoneurons from a SMARD1 mouse model that are insensitive to treatment with low dose PEGylated IGF1

por Krieger, Frank, Metzger, Friedrich, Jablonka, Sibylle
Publicado 2014

Therapy development for spinal muscular atrophy: perspectives for muscular dystrophies and neurodegenerative disorders

por Jablonka, Sibylle, Hennlein, Luisa, Sendtner, Michael
Publicado 2022

Defective Ca(2+) channel clustering in axon terminals disturbs excitability in motoneurons in spinal muscular atrophy

por Jablonka, Sibylle, Beck, Marcus, Lechner, Barbara Dorothea, Mayer, Christine, Sendtner, Michael
Publicado 2007

Presynaptic Localization of Smn and hnRNP R in Axon Terminals of Embryonic and Postnatal Mouse Motoneurons

por Dombert, Benjamin, Sivadasan, Rajeeve, Simon, Christian M., Jablonka, Sibylle, Sendtner, Michael
Publicado 2014

Lectin-based Isolation and Culture of Mouse Embryonic Motoneurons

por Conrad, Rebecca, Jablonka, Sibylle, Sczepan, Teresa, Sendtner, Michael, Wiese, Stefan, Klausmeyer, Alice
Publicado 2011

An open source tool for automatic spatiotemporal assessment of calcium transients and local ‘signal-close-to-noise’ activity in calcium imaging data

por Prada, Juan, Sasi, Manju, Martin, Corinna, Jablonka, Sibylle, Dandekar, Thomas, Blum, Robert
Publicado 2018

Nifedipine Ameliorates Cellular Differentiation Defects of Smn-Deficient Motor Neurons and Enhances Neuromuscular Transmission in SMA Mice

por Tejero, Rocio, Alsakkal, Mohammad, Hennlein, Luisa, Lopez-Cabello, Ana M., Jablonka, Sibylle, Tabares, Lucia
Publicado 2023

Missense mutation in the tubulin-specific chaperone E (Tbce) gene in the mouse mutant progressive motor neuronopathy, a model of human motoneuron disease

por Bömmel, Heike, Xie, Gang, Rossoll, Wilfried, Wiese, Stefan, Jablonka, Sibylle, Boehm, Thomas, Sendtner, Michael
Publicado 2002

BDNF/trkB Induction of Calcium Transients through Ca(v)2.2 Calcium Channels in Motoneurons Corresponds to F-actin Assembly and Growth Cone Formation on β2-Chain Laminin (221)

por Dombert, Benjamin, Balk, Stefanie, Lüningschrör, Patrick, Moradi, Mehri, Sivadasan, Rajeeve, Saal-Bauernschubert, Lena, Jablonka, Sibylle
Publicado 2017

Smn, the spinal muscular atrophy–determining gene product, modulates axon growth and localization of β-actin mRNA in growth cones of motoneurons

por Rossoll, Wilfried, Jablonka, Sibylle, Andreassi, Catia, Kröning, Ann-Kathrin, Karle, Kathrin, Monani, Umrao R., Sendtner, Michael
Publicado 2003

Pegylated Insulin-Like Growth Factor 1 attenuates Hair Cell Loss and promotes Presynaptic Maintenance of Medial Olivocochlear Cholinergic Fibers in the Cochlea of the Progressive M...

por Bieniussa, Linda, Kahraman, Baran, Skornicka, Johannes, Schulte, Annemarie, Voelker, Johannes, Jablonka, Sibylle, Hagen, Rudolf, Rak, Kristen
Publicado 2022

Axonal and dendritic localization of mRNAs for glycogen-metabolizing enzymes in cultured rodent neurons

por Pfeiffer-Guglielmi, Brigitte, Dombert, Benjamin, Jablonka, Sibylle, Hausherr, Vanessa, van Thriel, Christoph, Schöbel, Nicole, Jansen, Ralf-Peter
Publicado 2014

Interaction of 7SK with the Smn complex modulates snRNP production

por Ji, Changhe, Bader, Jakob, Ramanathan, Pradhipa, Hennlein, Luisa, Meissner, Felix, Jablonka, Sibylle, Mann, Matthias, Fischer, Utz, Sendtner, Michael, Briese, Michael
Publicado 2021

Impaired dynamic interaction of axonal endoplasmic reticulum and ribosomes contributes to defective stimulus–response in spinal muscular atrophy

por Deng, Chunchu, Reinhard, Sebastian, Hennlein, Luisa, Eilts, Janna, Sachs, Stefan, Doose, Sören, Jablonka, Sibylle, Sauer, Markus, Moradi, Mehri, Sendtner, Michael
Publicado 2022

Loss of Tdp-43 disrupts the axonal transcriptome of motoneurons accompanied by impaired axonal translation and mitochondria function

por Briese, Michael, Saal-Bauernschubert, Lena, Lüningschrör, Patrick, Moradi, Mehri, Dombert, Benjamin, Surrey, Verena, Appenzeller, Silke, Deng, Chunchu, Jablonka, Sibylle, Sendtner, Michael
Publicado 2020

Loss of full-length hnRNP R isoform impairs DNA damage response in motoneurons by inhibiting Yb1 recruitment to chromatin

por Ghanawi, Hanaa, Hennlein, Luisa, Zare, Abdolhossein, Bader, Jakob, Salehi, Saeede, Hornburg, Daniel, Ji, Changhe, Sivadasan, Rajeeve, Drepper, Carsten, Meissner, Felix, Mann, Matthias, Jablonka, Sibylle, Briese, Michael, Sendtner, Michael
Publicado 2021

A transgene carrying an A2G missense mutation in the SMN gene modulates phenotypic severity in mice with severe (type I) spinal muscular atrophy

por Monani, Umrao R., Pastore, Matthew T., Gavrilina, Tatiana O., Jablonka, Sibylle, Le, Thanh T., Andreassi, Catia, DiCocco, Jennifer M., Lorson, Christian, Androphy, Elliot J., Sendtner, Michael, Podell, Michael, Burghes, Arthur H.M.
Publicado 2003

Plastin 3 rescues cell surface translocation and activation of TrkB in spinal muscular atrophy

por Hennlein, Luisa, Ghanawi, Hanaa, Gerstner, Florian, Palominos García, Eduardo, Yildirim, Ezgi, Saal-Bauernschubert, Lena, Moradi, Mehri, Deng, Chunchu, Klein, Teresa, Appenzeller, Silke, Sauer, Markus, Briese, Michael, Simon, Christian, Sendtner, Michael, Jablonka, Sibylle
Publicado 2023

R-Roscovitine Improves Motoneuron Function in Mouse Models for Spinal Muscular Atrophy

por Tejero, Rocio, Balk, Stefanie, Franco-Espin, Julio, Ojeda, Jorge, Hennlein, Luisa, Drexl, Hans, Dombert, Benjamin, Clausen, Jan-Dierk, Torres-Benito, Laura, Saal-Bauernschubert, Lena, Blum, Robert, Briese, Michael, Appenzeller, Silke, Tabares, Lucia, Jablonka, Sibylle
Publicado 2020