Peroxin-Dependent Targeting of a Lipid Droplet-Destined Membrane Protein to ER-subdomains

por Schrul, Bianca, Kopito, Ron R.
Publicado 2016

Protein misfolding specifies recruitment to cytoplasmic inclusion bodies

por Bersuker, Kirill, Brandeis, Michael, Kopito, Ron R.
Publicado 2016

Aggresomes: A Cellular Response to Misfolded Proteins

por Johnston, Jennifer A., Ward, Cristina L., Kopito, Ron R.
Publicado 1998

RPL26/uL24 UFMylation is essential for ribosome-associated quality control at the endoplasmic reticulum

por Scavone, Francesco, Gumbin, Samantha C., DaRosa, Paul A., Kopito, Ron R.
Publicado 2023

RPL26/uL24 UFMylation is essential for ribosome-associated quality control at the endoplasmic reticulum

por Scavone, Francesco, Gumbin, Samantha C., Da Rosa, Paul A., Kopito, Ron R.
Publicado 2023

Simultaneous Measurement of Amyloid Fibril Formation by Dynamic Light Scattering and Fluorescence Reveals Complex Aggregation Kinetics

por Streets, Aaron M., Sourigues, Yannick, Kopito, Ron R., Melki, Ronald, Quake, Stephen R.
Publicado 2013

Perturbation of the Hematopoietic System during Embryonic Liver Development Due to Disruption of Polyubiquitin Gene Ubc in Mice

por Ryu, Kwon-Yul, Park, Hyejin, Rossi, Derrick J., Weissman, Irving L., Kopito, Ron R.
Publicado 2012

Prion-like transmission of neuronal huntingtin aggregates to phagocytic glia in the Drosophila brain

por Pearce, Margaret M.P., Spartz, Ellen J., Hong, Weizhe, Luo, Liqun, Kopito, Ron R.
Publicado 2015

Ubiquitin Accumulation on Disease Associated Protein Aggregates Is Correlated with Nuclear Ubiquitin Depletion, Histone De-Ubiquitination and Impaired DNA Damage Response

por Ben Yehuda, Adi, Risheq, Marwa, Novoplansky, Ofra, Bersuker, Kirill, Kopito, Ron R., Goldberg, Michal, Brandeis, Michael
Publicado 2017

Subversion of Cellular Autophagosomal Machinery by RNA Viruses

por Jackson, William T, Giddings, Thomas H, Taylor, Matthew P, Mulinyawe, Sara, Rabinovitch, Marlene, Kopito, Ron R, Kirkegaard, Karla
Publicado 2005

Small molecule correctors divert CFTR-F508del from ERAD by stabilizing sequential folding states

por Riepe, Celeste, Wąchalska, Magda, Deol, Kirandeep K., Amaya, Anais K., Porteus, Matthew H., Olzmann, James A., Kopito, Ron R.
Publicado 2023

Unassembled CD147 is an endogenous endoplasmic reticulum–associated degradation substrate

por Tyler, Ryan E., Pearce, Margaret M. P., Shaler, Thomas A., Olzmann, James A., Greenblatt, Ethan J., Kopito, Ron R.
Publicado 2012

Indirect inhibition of 26S proteasome activity in a cellular model of Huntington’s disease

por Hipp, Mark S., Patel, Chetan N., Bersuker, Kirill, Riley, Brigit E., Kaiser, Stephen E., Shaler, Thomas A., Brandeis, Michael, Kopito, Ron R.
Publicado 2012

Protein misfolding in neurodegenerative diseases: implications and strategies

por Sweeney, Patrick, Park, Hyunsun, Baumann, Marc, Dunlop, John, Frydman, Judith, Kopito, Ron, McCampbell, Alexander, Leblanc, Gabrielle, Venkateswaran, Anjli, Nurmi, Antti, Hodgson, Robert
Publicado 2017

A non‐canonical scaffold‐type E3 ligase complex mediates protein UFMylation

por Peter, Joshua J, Magnussen, Helge M, DaRosa, Paul A, Millrine, David, Matthews, Stephen P, Lamoliatte, Frederic, Sundaramoorthy, Ramasubramanian, Kopito, Ron R, Kulathu, Yogesh
Publicado 2022

Phagocytic glia are obligatory intermediates in transmission of mutant huntingtin aggregates across neuronal synapses

por Donnelly, Kirby M, DeLorenzo, Olivia R, Zaya, Aprem DA, Pisano, Gabrielle E, Thu, Wint M, Luo, Liqun, Kopito, Ron R, Panning Pearce, Margaret M
Publicado 2020

PEX19 Coordinates Neutral Lipid Storage in Cells in a Peroxisome-Independent Fashion

por Lyschik, Sven, Lauer, Anna A., Roth, Tanja, Janitschke, Daniel, Hollander, Markus, Will, Thorsten, Hartmann, Tobias, Kopito, Ron R., Helms, Volkhard, Grimm, Marcus O. W., Schrul, Bianca
Publicado 2022

The herpesvirus UL49.5 protein hijacks a cellular C-degron pathway to drive TAP transporter degradation

por Wąhalska, Magda, Riepe, Celeste, Ślusarz, Magdalena J., Graul, Małgorzata, Borowski, Lukasz S., Qiao, Wenjie, Foltynska, Michalina, Carette, Jan E., Bieńkowska-Szewczyk, Krystyna, Szczesny, Roman J., Kopito, Ron R., Lipińska, Andrea D.
Publicado 2023

Defining human ERAD networks through an integrative mapping strategy

por Christianson, John C., Olzmann, James A., Shaler, Thomas A., Sowa, Mathew E., Bennett, Eric J., Richter, Caleb M., Tyler, Ryan E., Greenblatt, Ethan J., Harper, J. Wade, Kopito, Ron R.
Publicado 2011

Ubiquitin accumulation in autophagy-deficient mice is dependent on the Nrf2-mediated stress response pathway: a potential role for protein aggregation in autophagic substrate selec...

por Riley, Brigit E., Kaiser, Stephen E., Shaler, Thomas A., Ng, Aylwin C.Y., Hara, Taichi, Hipp, Mark S., Lage, Kasper, Xavier, Ramnik J., Ryu, Kwon-Yul, Taguchi, Keiko, Yamamoto, Masayuki, Tanaka, Keiji, Mizushima, Noboru, Komatsu, Masaaki, Kopito, Ron R.
Publicado 2010