Mucus Aberrant Properties in CF: Insights from Cells and Animal Models

por Ehre, Camille, Hansson, Gunnar C., Thornton, David J., Ostedgaard, Lynda S.
Publicado 2023

Bovine AAV Transcytosis Inhibition by Tannic Acid Results in Functional Expression of CFTR in Vitro and Altered Bio-Distribution in Vivo

por Di Pasquale, Giovanni, Ostedgaard, Lynda, Vermeer, Daniel, Swaim, William D., Karp, Philip, Chiorini, John A.
Publicado 2011

Mutating the Conserved Q-loop Glutamine 1291 Selectively Disrupts Adenylate Kinase-dependent Channel Gating of the ATP-binding Cassette (ABC) Adenylate Kinase Cystic Fibrosis Trans...

por Dong, Qian, Ernst, Sarah E., Ostedgaard, Lynda S., Shah, Viral S., Ver Heul, Amanda R., Welsh, Michael J., Randak, Christoph O.
Publicado 2015

Alteration of protein function by a silent polymorphism linked to tRNA abundance

por Kirchner, Sebastian, Cai, Zhiwei, Rauscher, Robert, Kastelic, Nicolai, Anding, Melanie, Czech, Andreas, Kleizen, Bertrand, Ostedgaard, Lynda S., Braakman, Ineke, Sheppard, David N., Ignatova, Zoya
Publicado 2017

Early Pathogenesis of Cystic Fibrosis Gallbladder Disease in a Porcine Model

por Zarei, Keyan, Stroik, Mallory R., Gansemer, Nick D., Thurman, Andrew L., Ostedgaard, Lynda S., Ernst, Sarah E., Thornell, Ian M., Powers, Linda S., Pezzulo, Alejandro A., Meyerholz, David K., Stoltz, David A.
Publicado 2020

Widespread airway distribution and short-term phenotypic correction of cystic fibrosis pigs following aerosol delivery of piggyBac/adenovirus

por Cooney, Ashley L, Singh, Brajesh K, Loza, Laura Marquez, Thornell, Ian M, Hippee, Camilla E, Powers, Linda S, Ostedgaard, Lynda S, Meyerholz, David K, Wohlford-Lenane, Chris, Stoltz, David A, B. McCray, Paul, Sinn, Patrick L
Publicado 2018

Motile cilia of human airway epithelia contain hedgehog signaling components that mediate noncanonical hedgehog signaling

por Mao, Suifang, Shah, Alok S., Moninger, Thomas O., Ostedgaard, Lynda S., Lu, Lin, Tang, Xiao Xiao, Thornell, Ian M., Reznikov, Leah R., Ernst, Sarah E., Karp, Philip H., Tan, Ping, Keshavjee, Shaf, Abou Alaiwa, Mahmoud H., Welsh, Michael J.
Publicado 2018

Lack of airway submucosal glands impairs respiratory host defenses

por Ostedgaard, Lynda S, Price, Margaret P, Whitworth, Kristin M, Abou Alaiwa, Mahmoud H, Fischer, Anthony J, Warrier, Akshaya, Samuel, Melissa, Spate, Lee D, Allen, Patrick D, Hilkin, Brieanna M, Romano Ibarra, Guillermo S, Ortiz Bezara, Miguel E, Goodell, Brian J, Mather, Steven E, Powers, Linda S, Stroik, Mallory R, Gansemer, Nicholas D, Hippee, Camilla E, Zarei, Keyan, Goeken, J Adam, Businga, Thomas R, Hoffman, Eric A, Meyerholz, David K, Prather, Randall S, Stoltz, David A, Welsh, Michael J
Publicado 2020