Mucociliary Clearance in Mice Measured by Tracking Trans-tracheal Fluorescence of Nasally Aerosolized Beads

por Rogers, Troy D., Ostrowski, Lawrence E., Livraghi-Butrico, Alessandra, Button, Brian, Grubb, Barbara R.
Publicado 2018

Restoring ciliary function to differentiated Primary Ciliary Dyskinesia cells with a lentiviral vector

por Ostrowski, Lawrence E, Yin, Weining, Patel, Manij, Sechelski, John, Rogers, Troy, Burns, Kimberlie, Grubb, Barbara R, Olsen, John C
Publicado 2014

Induction of ciliary orientation by matrix patterning and characterization of mucociliary transport

por Sears, Patrick R., Bustamante-Marin, Ximena M., Gong, Henry, Markovetz, Matthew R., Superfine, Richard, Hill, David B., Ostrowski, Lawrence E.
Publicado 2021

Cryo-electron tomography reveals ciliary defects underlying human RSPH1 primary ciliary dyskinesia

por Lin, Jianfeng, Yin, Weining, Smith, Maria C., Song, Kangkang, Leigh, Margaret W., Zariwala, Maimoona A., Knowles, Michael R., Ostrowski, Lawrence E., Nicastro, Daniela
Publicado 2014

Voltage-dependent Anion Channel-1 (VDAC-1) Contributes to ATP Release and Cell Volume Regulation in Murine Cells

por Okada, Seiko F., O'Neal, Wanda K., Huang, Pingbo, Nicholas, Robert A., Ostrowski, Lawrence E., Craigen, William J., Lazarowski, Eduardo R., Boucher, Richard C.
Publicado 2004

Regional Differences in Mucociliary Clearance in the Upper and Lower Airways

por Rogers, Troy D., Button, Brian, Kelada, Samir N. P., Ostrowski, Lawrence E., Livraghi-Butrico, Alessandra, Gutay, Mark I., Esther, Charles R., Grubb, Barbara R.
Publicado 2022

Mucolytic treatment of chronic rhinosinusitis in a murine model of primary ciliary dyskinesia

por Yin, Weining, Golliher, Hannah L., Ferguson, Amy J., Kimbell, Julia S., Livraghi-Butrico, Alessandra, Rogers, Troy D., Grubb, Barbara R., Kimple, Adam J., Ostrowski, Lawrence E.
Publicado 2023

Structural insights into the cause of human RSPH4A primary ciliary dyskinesia

por Zhao, Yanhe, Pinskey, Justine, Lin, Jianfeng, Yin, Weining, Sears, Patrick R., Daniels, Leigh A., Zariwala, Maimoona A., Knowles, Michael R., Ostrowski, Lawrence E., Nicastro, Daniela
Publicado 2021

Identification of Genetic Variants in CFAP221 as a Cause of Primary Ciliary Dyskinesia

por Bustamante-Marin, Ximena M., Shapiro, Adam, Sears, Patrick R., Charng, Wu-Lin, Conrad, Donald F., Leigh, Margaret W., Knowles, Michael R., Ostrowski, Lawrence E., Zariwala, Maimoona A.
Publicado 2019

Expression of a Truncated Form of ODAD1 Associated with an Unusually Mild Primary Ciliary Dyskinesia Phenotype

por Ostrowski, Lawrence E., Yin, Weining, Smith, Amanda J., Sears, Patrick R., Bustamante-Marin, Ximena M., Dang, Hong, Hildebrandt, Friedhelm, Daniels, Leigh Anne, Capps, Nicole A., Sullivan, Kelli M., Leigh, Margaret W., Zariwala, Maimoona A., Knowles, Michael R.
Publicado 2022

Mutation of CFAP57, a protein required for the asymmetric targeting of a subset of inner dynein arms in Chlamydomonas, causes primary ciliary dyskinesia

por Bustamante-Marin, Ximena M., Horani, Amjad, Stoyanova, Mihaela, Charng, Wu-Lin, Bottier, Mathieu, Sears, Patrick R., Yin, Wei-Ning, Daniels, Leigh Anne, Bowen, Hailey, Conrad, Donald F., Knowles, Michael R., Ostrowski, Lawrence E., Zariwala, Maimoona A., Dutcher, Susan K.
Publicado 2020