The relation between sarcomere energetics and the rate of isometric tension relaxation in healthy and diseased cardiac muscle

por Vitale, Giulia, Ferrantini, Cecilia, Piroddi, Nicoletta, Scellini, Beatrice, Pioner, Josè Manuel, Colombini, Barbara, Tesi, Chiara, Poggesi, Corrado
Publicado 2019

Mavacamten has a differential impact on force generation in myofibrils from rabbit psoas and human cardiac muscle

por Scellini, Beatrice, Piroddi, Nicoletta, Dente, Marica, Vitale, Giulia, Pioner, Josè Manuel, Coppini, Raffaele, Ferrantini, Cecilia, Poggesi, Corrado, Tesi, Chiara
Publicado 2021

R4496C RyR2 mutation impairs atrial and ventricular contractility

por Ferrantini, Cecilia, Coppini, Raffaele, Scellini, Beatrice, Ferrara, Claudia, Pioner, Josè Manuel, Mazzoni, Luca, Priori, Silvia, Cerbai, Elisabetta, Tesi, Chiara, Poggesi, Corrado
Publicado 2016

Advances in Stem Cell Modeling of Dystrophin-Associated Disease: Implications for the Wider World of Dilated Cardiomyopathy

por Pioner, Josè Manuel, Fornaro, Alessandra, Coppini, Raffaele, Ceschia, Nicole, Sacconi, Leonardo, Donati, Maria Alice, Favilli, Silvia, Poggesi, Corrado, Olivotto, Iacopo, Ferrantini, Cecilia
Publicado 2020

A Novel Method of Isolating Myofibrils From Primary Cardiomyocyte Culture Suitable for Myofibril Mechanical Study

por Woulfe, Kathleen C., Ferrara, Claudia, Pioner, Jose Manuel, Mahaffey, Jennifer H., Coppini, Raffaele, Scellini, Beatrice, Ferrantini, Cecilia, Piroddi, Nicoletta, Tesi, Chiari, Poggesi, Corrado, Jeong, Mark
Publicado 2019

Genotype-Driven Pathogenesis of Atrial Fibrillation in Hypertrophic Cardiomyopathy: The Case of Different TNNT2 Mutations

por Pioner, Josè Manuel, Vitale, Giulia, Gentile, Francesca, Scellini, Beatrice, Piroddi, Nicoletta, Cerbai, Elisabetta, Olivotto, Iacopo, Tardiff, Jil, Coppini, Raffaele, Tesi, Chiara, Poggesi, Corrado, Ferrantini, Cecilia
Publicado 2022

IPSC derived cardiac fibroblasts of DMD patients show compromised actin microfilaments, metabolic shift and pro-fibrotic phenotype

por Soussi, Salwa, Savchenko, Lesia, Rovina, Davide, Iacovoni, Jason S., Gottinger, Andrea, Vialettes, Maxime, Pioner, Josè-Manuel, Farini, Andrea, Mallia, Sara, Rabino, Martina, Pompilio, Giulio, Parini, Angelo, Lairez, Olivier, Gowran, Aoife, Pizzinat, Nathalie
Publicado 2023

Correction: IPSC derived cardiac fibroblasts of DMD patients show compromised actin microfilaments, metabolic shift and pro-fibrotic phenotype

por Soussi, Salwa, Savchenko, Lesia, Rovina, Davide, Iacovoni, Jason S., Gottinger, Andrea, Vialettes, Maxime, Pioner, Josè-Manuel, Farini, Andrea, Mallia, Sara, Rabino, Martina, Pompilio, Giulio, Parini, Angelo, Lairez, Olivier, Gowran, Aoife, Pizzinat, Nathalie
Publicado 2023

Late sodium current inhibitors to treat exercise‐induced obstruction in hypertrophic cardiomyopathy: an in vitro study in human myocardium

por Ferrantini, Cecilia, Pioner, Josè Manuel, Mazzoni, Luca, Gentile, Francesca, Tosi, Benedetta, Rossi, Alessandra, Belardinelli, Luiz, Tesi, Chiara, Palandri, Chiara, Matucci, Rosanna, Cerbai, Elisabetta, Olivotto, Iacopo, Poggesi, Corrado, Mugelli, Alessandro, Coppini, Raffaele
Publicado 2018

Paradoxical prolongation of QT interval during exercise in patients with hypertrophic cardiomyopathy: cellular mechanisms and implications for diastolic function

por Coppini, Raffaele, Beltrami, Matteo, Doste, Ruben, Bueno-Orovio, Alfonso, Ferrantini, Cecilia, Vitale, Giulia, Pioner, Josè Manuel, Santini, Lorenzo, Argirò, Alessia, Berteotti, Martina, Mori, Fabio, Marchionni, Niccolò, Stefàno, Pierluigi, Cerbai, Elisabetta, Poggesi, Corrado, Olivotto, Iacopo
Publicado 2022

Isolation and Mechanical Measurements of Myofibrils from Human Induced Pluripotent Stem Cell-Derived Cardiomyocytes

por Pioner, Josè Manuel, Racca, Alice W., Klaiman, Jordan M., Yang, Kai-Chun, Guan, Xuan, Pabon, Lil, Muskheli, Veronica, Zaunbrecher, Rebecca, Macadangdang, Jesse, Jeong, Mark Y., Mack, David L., Childers, Martin K., Kim, Deok-Ho, Tesi, Chiara, Poggesi, Corrado, Murry, Charles E., Regnier, Michael
Publicado 2016

Pathogenesis of Hypertrophic Cardiomyopathy is Mutation Rather Than Disease Specific: A Comparison of the Cardiac Troponin T E163R and R92Q Mouse Models

por Ferrantini, Cecilia, Coppini, Raffaele, Pioner, Josè Manuel, Gentile, Francesca, Tosi, Benedetta, Mazzoni, Luca, Scellini, Beatrice, Piroddi, Nicoletta, Laurino, Annunziatina, Santini, Lorenzo, Spinelli, Valentina, Sacconi, Leonardo, De Tombe, Pieter, Moore, Rachel, Tardiff, Jil, Mugelli, Alessandro, Olivotto, Iacopo, Cerbai, Elisabetta, Tesi, Chiara, Poggesi, Corrado
Publicado 2017

Electrophysiological and Contractile Effects of Disopyramide in Patients With Obstructive Hypertrophic Cardiomyopathy: A Translational Study

por Coppini, Raffaele, Ferrantini, Cecilia, Pioner, Josè Manuel, Santini, Lorenzo, Wang, Zhinuo J., Palandri, Chiara, Scardigli, Marina, Vitale, Giulia, Sacconi, Leonardo, Stefàno, Pierluigi, Flink, Laura, Riedy, Katherine, Pavone, Francesco Saverio, Cerbai, Elisabetta, Poggesi, Corrado, Mugelli, Alessandro, Bueno-Orovio, Alfonso, Olivotto, Iacopo, Sherrid, Mark V.
Publicado 2019

Optical Investigation of Action Potential and Calcium Handling Maturation of hiPSC-Cardiomyocytes on Biomimetic Substrates

por Pioner, Josè Manuel, Santini, Lorenzo, Palandri, Chiara, Martella, Daniele, Lupi, Flavia, Langione, Marianna, Querceto, Silvia, Grandinetti, Bruno, Balducci, Valentina, Benzoni, Patrizia, Landi, Sara, Barbuti, Andrea, Ferrarese Lupi, Federico, Boarino, Luca, Sartiani, Laura, Tesi, Chiara, Mack, David L., Regnier, Michael, Cerbai, Elisabetta, Parmeggiani, Camilla, Poggesi, Corrado, Ferrantini, Cecilia, Coppini, Raffaele
Publicado 2019

Corrigendum: Calcium handling maturation and adaptation to increased substrate stiffness in human iPSC-derived cardiomyocytes: the impact of full-length dystrophin deficiency

por Pioner, Josè Manuel, Santini, Lorenzo, Palandri, Chiara, Langione, Marianna, Grandinetti, Bruno, Querceto, Silvia, Martella, Daniele, Mazzantini, Costanza, Scellini, Beatrice, Giammarino, Lucrezia, Lupi, Flavia, Mazzarotto, Francesco, Gowran, Aoife, Rovina, Davide, Santoro, Rosaria, Pompilio, Giulio, Tesi, Chiara, Parmeggiani, Camilla, Regnier, Michael, Cerbai, Elisabetta, Mack, David L., Poggesi, Corrado, Ferrantini, Cecilia, Coppini, Raffaele
Publicado 2023

Calcium handling maturation and adaptation to increased substrate stiffness in human iPSC-derived cardiomyocytes: The impact of full-length dystrophin deficiency

por Pioner, Josè Manuel, Santini, Lorenzo, Palandri, Chiara, Langione, Marianna, Grandinetti, Bruno, Querceto, Silvia, Martella, Daniele, Mazzantini, Costanza, Scellini, Beatrice, Giammarino, Lucrezia, Lupi, Flavia, Mazzarotto, Francesco, Gowran, Aoife, Rovina, Davide, Santoro, Rosaria, Pompilio, Giulio, Tesi, Chiara, Parmeggiani, Camilla, Regnier, Michael, Cerbai, Elisabetta, Mack, David L., Poggesi, Corrado, Ferrantini, Cecilia, Coppini, Raffaele
Publicado 2022

Slower Calcium Handling Balances Faster Cross-Bridge Cycling in Human MYBPC3 HCM

por Pioner, Josè Manuel, Vitale, Giulia, Steczina, Sonette, Langione, Marianna, Margara, Francesca, Santini, Lorenzo, Giardini, Francesco, Lazzeri, Erica, Piroddi, Nicoletta, Scellini, Beatrice, Palandri, Chiara, Schuldt, Maike, Spinelli, Valentina, Girolami, Francesca, Mazzarotto, Francesco, van der Velden, Jolanda, Cerbai, Elisabetta, Tesi, Chiara, Olivotto, Iacopo, Bueno-Orovio, Alfonso, Sacconi, Leonardo, Coppini, Raffaele, Ferrantini, Cecilia, Regnier, Michael, Poggesi, Corrado
Publicado 2023