Cholesterol homeostasis in the vertebrate retina: biology and pathobiology

por Ramachandra Rao, Sriganesh, Fliesler, Steven J.
Publicado 2021

Monitoring basal autophagy in the retina utilizing CAG-mRFP-EGFP-MAP1LC3B reporter mouse: technical and biological considerations

por Ramachandra Rao, Sriganesh, Fliesler, Steven J.
Publicado 2021

Lack of Overt Retinal Degeneration in a K42E Dhdds Knock-In Mouse Model of RP59

por Ramachandra Rao, Sriganesh, Fliesler, Steven J., Kotla, Pravallika, Nguyen, Mai N., Pittler, Steven J.
Publicado 2020

Morphological, biochemical, and transcriptomic characterization of iPSC-derived human RPE cells from normal and Smith-Lemli-Opitz syndrome patients

por Farkas, Michael H., Skelton, Lara A., Ramachandra-Rao, Sriganesh, Au, Elizabeth, Fliesler, Steven J.
Publicado 2022

Vertebrate Animal Models of RP59: Current Status and Future Prospects

por Fliesler, Steven J., Ramachandra Rao, Sriganesh, Nguyen, Mai N., KhalafAllah, Mahmoud Tawfik, Pittler, Steven J.
Publicado 2022

Prevention of Retinal Degeneration in a Rat Model of Smith-Lemli-Opitz Syndrome

por Fliesler, Steven J., Peachey, Neal S., Herron, Josi, Hines, Kelly M., Weinstock, Nadav I., Ramachandra Rao, Sriganesh, Xu, Libin
Publicado 2018

Retinal Degeneration Caused by Rod-Specific Dhdds Ablation Occurs without Concomitant Inhibition of Protein N-Glycosylation

por Ramachandra Rao, Sriganesh, Skelton, Lara A., Wu, Fuguo, Onysk, Agnieszka, Spolnik, Grzegorz, Danikiewicz, Witold, Butler, Mark C., Stacks, Delores A., Surmacz, Liliana, Mu, Xiuqian, Swiezewska, Ewa, Pittler, Steven J., Fliesler, Steven J.
Publicado 2020