Mitochondrial energetics is impaired in very long-chain acyl-CoA dehydrogenase deficiency and can be rescued by treatment with mitochondria-targeted electron scavengers

por Seminotti, Bianca, Leipnitz, Guilhian, Karunanidhi, Anuradha, Kochersperger, Catherine, Roginskaya, Vera Y, Basu, Shrabani, Wang, Yudong, Wipf, Peter, Van Houten, Bennett, Mohsen, Al-Walid, Vockley, Jerry
Publicado 2019

Evaluation of mitochondrial bioenergetics, dynamics, endoplasmic reticulum-mitochondria crosstalk, and reactive oxygen species in fibroblasts from patients with complex I deficienc...

por Leipnitz, Guilhian, Mohsen, Al-Walid, Karunanidhi, Anuradha, Seminotti, Bianca, Roginskaya, Vera Y., Markantone, Desiree M., Grings, Mateus, Mihalik, Stephanie J., Wipf, Peter, Van Houten, Bennett, Vockley, Jerry
Publicado 2018