Nitric oxide prevents Aft1 activation and metabolic remodeling in frataxin-deficient yeast

por Alsina, David, Ros, Joaquim, Tamarit, Jordi
Publicado 2017

Iron in Friedreich Ataxia: A Central Role in the Pathophysiology or an Epiphenomenon?

por Alsina, David, Purroy, Rosa, Ros, Joaquim, Tamarit, Jordi
Publicado 2018

Mitochondrial calcium signalling and neurodegenerative diseases

por Britti, Elena, Delaspre, Fabien, Tamarit, Jordi, Ros, Joaquim
Publicado 2018

Frataxin-deficient cardiomyocytes present an altered thiol-redox state which targets actin and pyruvate dehydrogenase

por Purroy, Rosa, Medina-Carbonero, Marta, Ros, Joaquim, Tamarit, Jordi
Publicado 2020

Frataxin‐deficient neurons and mice models of Friedreich ataxia are improved by TAT‐MTScs‐FXN treatment

por Britti, Elena, Delaspre, Fabien, Feldman, Anat, Osborne, Melissa, Greif, Hagar, Tamarit, Jordi, Ros, Joaquim
Publicado 2017

Evolution of an Iron-Detoxifying Protein: Eukaryotic and Rickettsia Frataxins Contain a Conserved Site Which Is Not Present in Their Bacterial Homologues

por Alves, Rui, Pazos-Gil, Maria, Medina-Carbonero, Marta, Sanz-Alcázar, Arabela, Delaspre, Fabien, Tamarit, Jordi
Publicado 2022

Mice harboring the FXN I151F pathological point mutation present decreased frataxin levels, a Friedreich ataxia-like phenotype, and mitochondrial alterations

por Medina-Carbonero, Marta, Sanz-Alcázar, Arabela, Britti, Elena, Delaspre, Fabien, Cabiscol, Elisa, Ros, Joaquim, Tamarit, Jordi
Publicado 2022