NorUDCA promotes degradation of α1-antitrypsin mutant Z protein by inducing autophagy through AMPK/ULK1 pathway

por Tang, Youcai, Blomenkamp, Keith S., Fickert, Peter, Trauner, Michael, Teckman, Jeffrey H.
Publicado 2018

AFM Imaging Reveals Topographic Diversity of Wild Type and Z Variant Polymers of Human α(1)-Proteinase Inhibitor

por Gaczynska, Maria, Karpowicz, Przemyslaw, Stuart, Christine E., Norton, Malgorzata G., Teckman, Jeffrey H., Marszal, Ewa, Osmulski, Pawel A.
Publicado 2016

Sarcopenia is associated with osteopenia and impaired quality of life in children with genetic intrahepatic cholestatic liver disease

por Boster, Julia M., Goodrich, Nathan P., Spino, Cathie, Loomes, Kathleen M., Alonso, Estella M., Kamath, Binita M., Sokol, Ronald J., Karpen, Saul, Miethke, Alexander, Shneider, Benjamin L., Molleston, Jean P., Kohli, Rohit, Horslen, Simon P., Rosenthal, Philip, Valentino, Pamela L., Teckman, Jeffrey H., Hangartner, Thomas N., Sundaram, Shikha S.
Publicado 2023

Nonfasted Liver Stiffness Correlates with Liver Disease Parameters and Portal Hypertension in Pediatric Cholestatic Liver Disease

por Shneider, Benjamin L., Goodrich, Nathan P., Ye, Wen, Sawyers, Cindy, Molleston, Jean P., Merion, Robert M., Leung, Daniel H., Karpen, Saul J., Kamath, Binita M., Cavallo, Laurel, Wang, Kasper, Teckman, Jeffrey H., Squires, James E., Sundaram, Shikha S., Rosenthal, Philip, Romero, Rene, Murray, Karen F., Loomes, Kathleen M., Jensen, M. Kyle, Bezerra, Jorge A., Bass, Lee M., Sokol, Ronald J., Magee, John C.
Publicado 2020