Emerging Concepts in Vector Development for Glial Gene Therapy: Implications for Leukodystrophies

por von Jonquieres, Georg, Rae, Caroline D., Housley, Gary D.
Publicado 2021

Loss of Central Auditory Processing in a Mouse Model of Canavan Disease

por von Jonquieres, Georg, Froud, Kristina E., Klugmann, Claudia B., Wong, Ann C. Y., Housley, Gary D., Klugmann, Matthias
Publicado 2014

Dual-function AAV gene therapy reverses late-stage Canavan disease pathology in mice

por Fröhlich, Dominik, Kalotay, Elizabeth, von Jonquieres, Georg, Bongers, Andre, Lee, Brendan, Suchowerska, Alexandra K., Housley, Gary D., Klugmann, Matthias
Publicado 2022

Recombinant Human Myelin-Associated Glycoprotein Promoter Drives Selective AAV-Mediated Transgene Expression in Oligodendrocytes

por von Jonquieres, Georg, Fröhlich, Dominik, Klugmann, Claudia B., Wen, Xin, Harasta, Anne E., Ramkumar, Roshini, Spencer, Ziggy H. T., Housley, Gary D., Klugmann, Matthias
Publicado 2016

Expression Pattern of the Aspartyl-tRNA Synthetase DARS in the Human Brain

por Fröhlich, Dominik, Suchowerska, Alexandra K., Voss, Carola, He, Ruojie, Wolvetang, Ernst, von Jonquieres, Georg, Simons, Cas, Fath, Thomas, Housley, Gary D., Klugmann, Matthias
Publicado 2018

Behavioral and Neurochemical Phenotyping of Mice Incapable of Homer1a Induction

por Datko, Michael C., Hu, Jia-Hua, Williams, Melanie, Reyes, Cindy M., Lominac, Kevin D., von Jonquieres, Georg, Klugmann, Matthias, Worley, Paul F., Szumlinski, Karen K.
Publicado 2017

Australian Scorpion Hormurus waigiensis Venom Fractions Show Broad Bioactivity through Modulation of Bio-Impedance and Cytosolic Calcium

por Housley, David M., Pinyon, Jeremy L., von Jonquieres, Georg, Perera, Chamini J., Smout, Michael, Liddell, Michael J., Jennings, Ernest A., Wilson, David, Housley, Gary D.
Publicado 2020

Glial Promoter Selectivity following AAV-Delivery to the Immature Brain

por von Jonquieres, Georg, Mersmann, Nadine, Klugmann, Claudia Bettina, Harasta, Anne Editha, Lutz, Beat, Teahan, Orla, Housley, Gary David, Fröhlich, Dominik, Krämer-Albers, Eva-Maria, Klugmann, Matthias
Publicado 2013

Noise-induced hearing loss vulnerability in type III intermediate filament peripherin gene knockout mice

por Cederholm, Jennie M. E., Parley, Kristina E., Perera, Chamini J., von Jonquieres, Georg, Pinyon, Jeremy L., Julien, Jean-Pierre, Ryugo, David K., Ryan, Allen F., Housley, Gary D.
Publicado 2022

Transgenic Analyses of Homer2 Function Within Nucleus Accumbens Subregions in the Regulation of Methamphetamine Reward and Reinforcement in Mice

por Brown, Chelsea N., Fultz, Elissa K., Ferdousian, Sami, Rogers, Sarina, Lustig, Elijah, Page, Ariana, Shahin, John R., Flaherty, Daniel M., Von Jonquieres, Georg, Bryant, Camron D., Kippin, Tod E., Szumlinski, Karen K.
Publicado 2020

Homers at the Interface between Reward and Pain

por Obara, Ilona, Goulding, Scott P., Gould, Adam T., Lominac, Kevin D., Hu, Jia-Hua, Zhang, Ping Wu, von Jonquieres, Georg, Dehoff, Marlin, Xiao, Bo, Seeburg, Peter H., Worley, Paul F., Klugmann, Matthias, Szumlinski, Karen K.
Publicado 2013

DKC1 is a transcriptional target of GATA1 and drives upregulation of telomerase activity in normal human erythroblasts

por Richards, Laura A., Kumari, Ashu, Knezevic, Kathy, Thoms, Julie AI, von Jonquieres, Georg, Napier, Christine E., Ali, Zara, O’Brien, Rosemary, Marks-Bluth, Jonathon, Maritz, Michelle F., Pickett, Hilda A, Morris, Jonathan, Pimanda, John E., MacKenzie, Karen L.
Publicado 2020

Uncoupling N-acetylaspartate from brain pathology: implications for Canavan disease gene therapy

por von Jonquieres, Georg, Spencer, Ziggy H. T., Rowlands, Benjamin D., Klugmann, Claudia B., Bongers, Andre, Harasta, Anne E., Parley, Kristina E., Cederholm, Jennie, Teahan, Orla, Pickford, Russell, Delerue, Fabien, Ittner, Lars M., Fröhlich, Dominik, McLean, Catriona A., Don, Anthony S., Schneider, Miriam, Housley, Gary D., Rae, Caroline D., Klugmann, Matthias
Publicado 2017