Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease

Erdheim-Chester disease (ECD) as a rare non-Langerhans histiocytosis has various clinical manifestations. It is characterized histologically by infiltration of every organ, more commonly bone, retroperitoneum, cardiovascular and CNS systems with foamy, lipid -laden macrophage. Pancreatic involvement...

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Autores principales: Rafiee, Moezedin Javad, Taylor, Jana, Hickeson, Marc, Friedrich, Matthias G., Chetrit, Michael
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2023
Materias:
Case Report
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10006724/
https://www.ncbi.nlm.nih.gov/pubmed/36915608
http://dx.doi.org/10.1016/j.radcr.2023.02.012
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author Rafiee, Moezedin Javad
Taylor, Jana
Hickeson, Marc
Friedrich, Matthias G.
Chetrit, Michael
author_facet Rafiee, Moezedin Javad
Taylor, Jana
Hickeson, Marc
Friedrich, Matthias G.
Chetrit, Michael
author_sort Rafiee, Moezedin Javad
collection PubMed
description Erdheim-Chester disease (ECD) as a rare non-Langerhans histiocytosis has various clinical manifestations. It is characterized histologically by infiltration of every organ, more commonly bone, retroperitoneum, cardiovascular and CNS systems with foamy, lipid -laden macrophage. Pancreatic involvement as a manifestation of this uncommon disease has very rarely been reported. Here we report a 73-year-old woman with ECD and pancreas involvement in CT, MRI and PET scans. We also aim to increase radiologist knowledge about considering ECD as a differential diagnosis for pancreas mass in the appropriate clinical situation.
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spelling pubmed-100067242023-03-12 Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease Rafiee, Moezedin Javad Taylor, Jana Hickeson, Marc Friedrich, Matthias G. Chetrit, Michael Radiol Case Rep Case Report Erdheim-Chester disease (ECD) as a rare non-Langerhans histiocytosis has various clinical manifestations. It is characterized histologically by infiltration of every organ, more commonly bone, retroperitoneum, cardiovascular and CNS systems with foamy, lipid -laden macrophage. Pancreatic involvement as a manifestation of this uncommon disease has very rarely been reported. Here we report a 73-year-old woman with ECD and pancreas involvement in CT, MRI and PET scans. We also aim to increase radiologist knowledge about considering ECD as a differential diagnosis for pancreas mass in the appropriate clinical situation. Elsevier 2023-03-04 /pmc/articles/PMC10006724/ /pubmed/36915608 http://dx.doi.org/10.1016/j.radcr.2023.02.012 Text en © 2023 The Authors. Published by Elsevier Inc. on behalf of University of Washington. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Rafiee, Moezedin Javad
Taylor, Jana
Hickeson, Marc
Friedrich, Matthias G.
Chetrit, Michael
Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease
title Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease
title_full Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease
title_fullStr Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease
title_full_unstemmed Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease
title_short Pancreatic involvement in Erdheim-Chester disease: Rare presentation of a rare disease
title_sort pancreatic involvement in erdheim-chester disease: rare presentation of a rare disease
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10006724/
https://www.ncbi.nlm.nih.gov/pubmed/36915608
http://dx.doi.org/10.1016/j.radcr.2023.02.012
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