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Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?

Right-to-left shunt due to abnormal systemic venous drainage to the left heart is among the causes of hypoxemia following Fontan operation. There are conflicting data regarding the closure of the venovenous collaterals (VVCs) post-Fontan, showing decreased survival in older patients. In a child with...

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Autores principales: El-Khouri, Maya, Arabi, Mariam, El Rassi, Issam, Bulbul, Ziad, Sawaya, Fadi, Bitar, Fadi
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2022
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10015390/
https://www.ncbi.nlm.nih.gov/pubmed/36935823
http://dx.doi.org/10.4103/apc.apc_193_21
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author El-Khouri, Maya
Arabi, Mariam
El Rassi, Issam
Bulbul, Ziad
Sawaya, Fadi
Bitar, Fadi
author_facet El-Khouri, Maya
Arabi, Mariam
El Rassi, Issam
Bulbul, Ziad
Sawaya, Fadi
Bitar, Fadi
author_sort El-Khouri, Maya
collection PubMed
description Right-to-left shunt due to abnormal systemic venous drainage to the left heart is among the causes of hypoxemia following Fontan operation. There are conflicting data regarding the closure of the venovenous collaterals (VVCs) post-Fontan, showing decreased survival in older patients. In a child with visceral heterotaxy, we describe a rare fistula draining a right-sided hepatic vein into hepatic venous plexus and a right-sided pulmonary venous atrium. The patient presented with severe hypoxemia post-Fontan and underwent fistula occlusion with AMPLATZER™ Vascular Plug II, successfully improving hemodynamic status with resolution of the hypoxemia. Younger patients with cyanosis due to VVCs may benefit from percutaneous occlusion post-Fontan.
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spelling pubmed-100153902023-03-16 Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation? El-Khouri, Maya Arabi, Mariam El Rassi, Issam Bulbul, Ziad Sawaya, Fadi Bitar, Fadi Ann Pediatr Cardiol Case Report Right-to-left shunt due to abnormal systemic venous drainage to the left heart is among the causes of hypoxemia following Fontan operation. There are conflicting data regarding the closure of the venovenous collaterals (VVCs) post-Fontan, showing decreased survival in older patients. In a child with visceral heterotaxy, we describe a rare fistula draining a right-sided hepatic vein into hepatic venous plexus and a right-sided pulmonary venous atrium. The patient presented with severe hypoxemia post-Fontan and underwent fistula occlusion with AMPLATZER™ Vascular Plug II, successfully improving hemodynamic status with resolution of the hypoxemia. Younger patients with cyanosis due to VVCs may benefit from percutaneous occlusion post-Fontan. Wolters Kluwer - Medknow 2022 2023-01-06 /pmc/articles/PMC10015390/ /pubmed/36935823 http://dx.doi.org/10.4103/apc.apc_193_21 Text en Copyright: © 2023 Annals of Pediatric Cardiology https://creativecommons.org/licenses/by-nc-sa/4.0/This is an open access journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.
spellingShingle Case Report
El-Khouri, Maya
Arabi, Mariam
El Rassi, Issam
Bulbul, Ziad
Sawaya, Fadi
Bitar, Fadi
Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?
title Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?
title_full Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?
title_fullStr Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?
title_full_unstemmed Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?
title_short Transcatheter occlusion of a hepatic vein-to-left atrium fistula: Should we close venovenous collateral vessels following Fontan operation?
title_sort transcatheter occlusion of a hepatic vein-to-left atrium fistula: should we close venovenous collateral vessels following fontan operation?
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10015390/
https://www.ncbi.nlm.nih.gov/pubmed/36935823
http://dx.doi.org/10.4103/apc.apc_193_21
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