Portopulmonary hypertension: Success with combined medical treatment

Portopulmonary hypertension is an uncommon disease associated with high morbidity and mortality, so its early diagnosis and treatment are essential. We report here the case of a 57‐year‐old man with portopulmonary hypertension caused by chronic hepatosplenic schistosomiasis and also liver cirrhosis...

Descripción completa

Detalles Bibliográficos
Autores principales: Hernández, María, Esteban, Violeta, Ruiz, Paloma, Boira, Ignacio, Wickmann, Phillip, Sancho‐Chust, José N., Gil, Joan
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley & Sons, Ltd 2023
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10020675/
https://www.ncbi.nlm.nih.gov/pubmed/36935896
http://dx.doi.org/10.1002/rcr2.1114
_version_ 1784908314156466176
author Hernández, María
Esteban, Violeta
Ruiz, Paloma
Boira, Ignacio
Wickmann, Phillip
Sancho‐Chust, José N.
Gil, Joan
author_facet Hernández, María
Esteban, Violeta
Ruiz, Paloma
Boira, Ignacio
Wickmann, Phillip
Sancho‐Chust, José N.
Gil, Joan
author_sort Hernández, María
collection PubMed
description Portopulmonary hypertension is an uncommon disease associated with high morbidity and mortality, so its early diagnosis and treatment are essential. We report here the case of a 57‐year‐old man with portopulmonary hypertension caused by chronic hepatosplenic schistosomiasis and also liver cirrhosis due to hepatitis C and alcoholism. As well as treating both diseases, portopulmonary hypertension was successfully managed with tadalafil and macitentan as maintenance therapy. This case reminds clinicians that pulmonary hypertension can be multifactorial, a good diagnosis and a multidisciplinary treatment can lead to improved prognosis.
format Online
Article
Text
id pubmed-10020675
institution National Center for Biotechnology Information
language English
publishDate 2023
publisher John Wiley & Sons, Ltd
record_format MEDLINE/PubMed
spelling pubmed-100206752023-03-18 Portopulmonary hypertension: Success with combined medical treatment Hernández, María Esteban, Violeta Ruiz, Paloma Boira, Ignacio Wickmann, Phillip Sancho‐Chust, José N. Gil, Joan Respirol Case Rep Case Reports Portopulmonary hypertension is an uncommon disease associated with high morbidity and mortality, so its early diagnosis and treatment are essential. We report here the case of a 57‐year‐old man with portopulmonary hypertension caused by chronic hepatosplenic schistosomiasis and also liver cirrhosis due to hepatitis C and alcoholism. As well as treating both diseases, portopulmonary hypertension was successfully managed with tadalafil and macitentan as maintenance therapy. This case reminds clinicians that pulmonary hypertension can be multifactorial, a good diagnosis and a multidisciplinary treatment can lead to improved prognosis. John Wiley & Sons, Ltd 2023-03-16 /pmc/articles/PMC10020675/ /pubmed/36935896 http://dx.doi.org/10.1002/rcr2.1114 Text en © 2023 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology. https://creativecommons.org/licenses/by/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by/4.0/ (https://creativecommons.org/licenses/by/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Reports
Hernández, María
Esteban, Violeta
Ruiz, Paloma
Boira, Ignacio
Wickmann, Phillip
Sancho‐Chust, José N.
Gil, Joan
Portopulmonary hypertension: Success with combined medical treatment
title Portopulmonary hypertension: Success with combined medical treatment
title_full Portopulmonary hypertension: Success with combined medical treatment
title_fullStr Portopulmonary hypertension: Success with combined medical treatment
title_full_unstemmed Portopulmonary hypertension: Success with combined medical treatment
title_short Portopulmonary hypertension: Success with combined medical treatment
title_sort portopulmonary hypertension: success with combined medical treatment
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10020675/
https://www.ncbi.nlm.nih.gov/pubmed/36935896
http://dx.doi.org/10.1002/rcr2.1114
work_keys_str_mv AT hernandezmaria portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment
AT estebanvioleta portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment
AT ruizpaloma portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment
AT boiraignacio portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment
AT wickmannphillip portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment
AT sanchochustjosen portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment
AT giljoan portopulmonaryhypertensionsuccesswithcombinedmedicaltreatment

Ejemplares similares