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Increased cardiac involvement in Fabry disease using blood-corrected native T1 mapping
Fabry disease (FD) is a rare lysosomal storage disorder resulting in myocardial sphingolipid accumulation which is detectable by cardiovascular magnetic resonance as low native T1. However, myocardial T1 contains signal from intramyocardial blood which affects variability and consequently measuremen...
Autores principales: | Nickander, Jannike, Cole, Ben, Nordin, Sabrina, Vijapurapu, Ravi, Steeds, Richard P., Moon, James C., Kellman, Peter, Ugander, Martin, Kozor, Rebecca |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Nature Publishing Group UK
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10023696/ https://www.ncbi.nlm.nih.gov/pubmed/36932097 http://dx.doi.org/10.1038/s41598-023-31211-9 |
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