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Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis
INTRODUCTION: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. CASE: A 29-year-old female at third trimester of twi...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10025273/ https://www.ncbi.nlm.nih.gov/pubmed/36950023 http://dx.doi.org/10.1016/j.rmcr.2023.101834 |
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author | Wong, Yen Shen Abidin, Zakhirati Zainol Musa, Aisya Natasya Kadir, Roqiah Fatmawati Abdul Johari, Bushra |
author_facet | Wong, Yen Shen Abidin, Zakhirati Zainol Musa, Aisya Natasya Kadir, Roqiah Fatmawati Abdul Johari, Bushra |
author_sort | Wong, Yen Shen |
collection | PubMed |
description | INTRODUCTION: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. CASE: A 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum. CONCLUSION: Clinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings. |
format | Online Article Text |
id | pubmed-10025273 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-100252732023-03-21 Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis Wong, Yen Shen Abidin, Zakhirati Zainol Musa, Aisya Natasya Kadir, Roqiah Fatmawati Abdul Johari, Bushra Respir Med Case Rep Case Report INTRODUCTION: Unilateral pulmonary artery agenesis (UPAA) is a rare congenital malformation of the pulmonary artery due to agenesis of the sixth aortic arch during embryogenesis. Diagnosis can be challenging due to variable clinical presentations. CASE: A 29-year-old female at third trimester of twin pregnancy presented with massive hemoptysis. Computed tomography angiogram (CTA) showed unilateral absence of the right pulmonary artery with multiple dilated tortuous bronchial arteries supplying the right lung. Selective embolization of the bronchial artery was performed post-partum. CONCLUSION: Clinicians should have a high clinical suspicion of collateral artery bleeding in patients who present with unexplained hemoptysis and typical UPAA radiographic findings. Elsevier 2023-03-10 /pmc/articles/PMC10025273/ /pubmed/36950023 http://dx.doi.org/10.1016/j.rmcr.2023.101834 Text en © 2023 Published by Elsevier Ltd. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Wong, Yen Shen Abidin, Zakhirati Zainol Musa, Aisya Natasya Kadir, Roqiah Fatmawati Abdul Johari, Bushra Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
title | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
title_full | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
title_fullStr | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
title_full_unstemmed | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
title_short | Unilateral pulmonary artery agenesis: An unusual cause of hemoptysis |
title_sort | unilateral pulmonary artery agenesis: an unusual cause of hemoptysis |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10025273/ https://www.ncbi.nlm.nih.gov/pubmed/36950023 http://dx.doi.org/10.1016/j.rmcr.2023.101834 |
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