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Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review

Erythromelalgia is a rare disease, involving pain, edema, redness, and hyperthermia in the limbs. It is extremely refractory to drugs, has no defined treatment, and causes psychological comorbidities in the patient. We describe a case of erythromelalgia involving a 17-year-old boy who had been suffe...

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Autores principales: Loureiro, Marcelo de Paula, Novais, Pietro Maran, Paulin, João Augusto Nocera, de Almeida, Daniel Benzecry, de Lemos, Arlindo Nascimento
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10026352/
https://www.ncbi.nlm.nih.gov/pubmed/36950140
http://dx.doi.org/10.1590/1677-5449.202200952
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author Loureiro, Marcelo de Paula
Novais, Pietro Maran
Paulin, João Augusto Nocera
de Almeida, Daniel Benzecry
de Lemos, Arlindo Nascimento
author_facet Loureiro, Marcelo de Paula
Novais, Pietro Maran
Paulin, João Augusto Nocera
de Almeida, Daniel Benzecry
de Lemos, Arlindo Nascimento
author_sort Loureiro, Marcelo de Paula
collection PubMed
description Erythromelalgia is a rare disease, involving pain, edema, redness, and hyperthermia in the limbs. It is extremely refractory to drugs, has no defined treatment, and causes psychological comorbidities in the patient. We describe a case of erythromelalgia involving a 17-year-old boy who had been suffering from the disease for almost 4 years prior to finding an effective treatment. A bilateral endoscopic lumbar sympathectomy was performed, limited to L2 and L3 resections. Four weeks after the procedure, the patient’s symptoms were significantly mitigated and at 8 months follow-up he remained almost asymptomatic. Endoscopic lumbar sympathectomy was an effective treatment for primary erythromelalgia in this teenager, with exceptional reduction of his symptoms.
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spelling pubmed-100263522023-03-21 Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review Loureiro, Marcelo de Paula Novais, Pietro Maran Paulin, João Augusto Nocera de Almeida, Daniel Benzecry de Lemos, Arlindo Nascimento J Vasc Bras Case Report Erythromelalgia is a rare disease, involving pain, edema, redness, and hyperthermia in the limbs. It is extremely refractory to drugs, has no defined treatment, and causes psychological comorbidities in the patient. We describe a case of erythromelalgia involving a 17-year-old boy who had been suffering from the disease for almost 4 years prior to finding an effective treatment. A bilateral endoscopic lumbar sympathectomy was performed, limited to L2 and L3 resections. Four weeks after the procedure, the patient’s symptoms were significantly mitigated and at 8 months follow-up he remained almost asymptomatic. Endoscopic lumbar sympathectomy was an effective treatment for primary erythromelalgia in this teenager, with exceptional reduction of his symptoms. Sociedade Brasileira de Angiologia e de Cirurgia Vascular (SBACV) 2023-03-10 /pmc/articles/PMC10026352/ /pubmed/36950140 http://dx.doi.org/10.1590/1677-5449.202200952 Text en Copyright© 2023 The authors. https://creativecommons.org/licenses/by/4.0/Copyright© 2023 The authors. This is an Open Access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original work is properly cited.
spellingShingle Case Report
Loureiro, Marcelo de Paula
Novais, Pietro Maran
Paulin, João Augusto Nocera
de Almeida, Daniel Benzecry
de Lemos, Arlindo Nascimento
Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
title Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
title_full Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
title_fullStr Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
title_full_unstemmed Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
title_short Endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
title_sort endoscopic lumbar sympathectomy as a treatment option for primary erythromelalgia - case report and review
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10026352/
https://www.ncbi.nlm.nih.gov/pubmed/36950140
http://dx.doi.org/10.1590/1677-5449.202200952
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