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A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung

Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing...

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Autores principales: Rath, Smruti, Dcunha, Nicholas Joseph, Bhan, Neel, Cox, Bettye, Adrish, Muhammad
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Elsevier 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10031536/
https://www.ncbi.nlm.nih.gov/pubmed/36970497
http://dx.doi.org/10.1016/j.rmcr.2023.101837
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author Rath, Smruti
Dcunha, Nicholas Joseph
Bhan, Neel
Cox, Bettye
Adrish, Muhammad
author_facet Rath, Smruti
Dcunha, Nicholas Joseph
Bhan, Neel
Cox, Bettye
Adrish, Muhammad
author_sort Rath, Smruti
collection PubMed
description Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma.
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spelling pubmed-100315362023-03-23 A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung Rath, Smruti Dcunha, Nicholas Joseph Bhan, Neel Cox, Bettye Adrish, Muhammad Respir Med Case Rep Case Report Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma. Elsevier 2023-03-13 /pmc/articles/PMC10031536/ /pubmed/36970497 http://dx.doi.org/10.1016/j.rmcr.2023.101837 Text en © 2023 The Authors. Published by Elsevier Ltd. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/).
spellingShingle Case Report
Rath, Smruti
Dcunha, Nicholas Joseph
Bhan, Neel
Cox, Bettye
Adrish, Muhammad
A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
title A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
title_full A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
title_fullStr A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
title_full_unstemmed A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
title_short A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
title_sort rare case of isolated thoracic al-amyloidoma causing complete atelectasis of the right lung
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10031536/
https://www.ncbi.nlm.nih.gov/pubmed/36970497
http://dx.doi.org/10.1016/j.rmcr.2023.101837
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