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A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung
Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing...
Autores principales: | , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Elsevier
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10031536/ https://www.ncbi.nlm.nih.gov/pubmed/36970497 http://dx.doi.org/10.1016/j.rmcr.2023.101837 |
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author | Rath, Smruti Dcunha, Nicholas Joseph Bhan, Neel Cox, Bettye Adrish, Muhammad |
author_facet | Rath, Smruti Dcunha, Nicholas Joseph Bhan, Neel Cox, Bettye Adrish, Muhammad |
author_sort | Rath, Smruti |
collection | PubMed |
description | Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma. |
format | Online Article Text |
id | pubmed-10031536 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Elsevier |
record_format | MEDLINE/PubMed |
spelling | pubmed-100315362023-03-23 A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung Rath, Smruti Dcunha, Nicholas Joseph Bhan, Neel Cox, Bettye Adrish, Muhammad Respir Med Case Rep Case Report Tumoral amyloidosis, or amyloidoma, is a benign, but rare form of amyloidosis that has been reported with a favorable prognosis following surgical resection in some case reports. We present a case of acute on chronic respiratory failure secondary to extensive growth of a thoracic amyloidoma causing atelectasis of the right lung. Our case patient had greater morbidity due to late presentation and extensive disease at diagnosis, precluding any surgical intervention. Radiation therapy and medical management were unsuccessful in reducing disease burden. Early diagnosis and detection are pivotal to improving survival in patients with isolated thoracic amyloidoma. Elsevier 2023-03-13 /pmc/articles/PMC10031536/ /pubmed/36970497 http://dx.doi.org/10.1016/j.rmcr.2023.101837 Text en © 2023 The Authors. Published by Elsevier Ltd. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the CC BY-NC-ND license (http://creativecommons.org/licenses/by-nc-nd/4.0/). |
spellingShingle | Case Report Rath, Smruti Dcunha, Nicholas Joseph Bhan, Neel Cox, Bettye Adrish, Muhammad A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
title | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
title_full | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
title_fullStr | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
title_full_unstemmed | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
title_short | A rare case of isolated thoracic AL-amyloidoma causing complete atelectasis of the right lung |
title_sort | rare case of isolated thoracic al-amyloidoma causing complete atelectasis of the right lung |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10031536/ https://www.ncbi.nlm.nih.gov/pubmed/36970497 http://dx.doi.org/10.1016/j.rmcr.2023.101837 |
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