Multiple complications of advanced IPF in an individual patient presentation

We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based treatment fo...

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Detalles Bibliográficos
Autores principales: Ledger, Thomas, Braude, Stanley
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley & Sons, Ltd 2023
Materias:
Case Reports
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10037082/
https://www.ncbi.nlm.nih.gov/pubmed/36970298
http://dx.doi.org/10.1002/rcr2.1118
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author Ledger, Thomas
Braude, Stanley
author_facet Ledger, Thomas
Braude, Stanley
author_sort Ledger, Thomas
collection PubMed
description We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based treatment for an acute exacerbation, we report a marked improvement with high‐dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non‐cardiac chest pain, as well as platypnoea‐orthodeoxia in those with positional dyspnoea.
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spelling pubmed-100370822023-03-25 Multiple complications of advanced IPF in an individual patient presentation Ledger, Thomas Braude, Stanley Respirol Case Rep Case Reports We report a patient with advanced idiopathic pulmonary fibrosis (IPF), who in a single presentation experienced three complications of the disease: an acute exacerbation, spontaneous pneumomediastinum, and platypnoea‐orthodeoxia syndrome. Despite there being no definitive evidence‐based treatment for an acute exacerbation, we report a marked improvement with high‐dose steroids. This case also highlights the importance in IPF patients of considering pneumomediastinum as a cause of non‐cardiac chest pain, as well as platypnoea‐orthodeoxia in those with positional dyspnoea. John Wiley & Sons, Ltd 2023-03-24 /pmc/articles/PMC10037082/ /pubmed/36970298 http://dx.doi.org/10.1002/rcr2.1118 Text en © 2023 The Authors. Respirology Case Reports published by John Wiley & Sons Australia, Ltd on behalf of The Asian Pacific Society of Respirology. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/) License, which permits use and distribution in any medium, provided the original work is properly cited, the use is non‐commercial and no modifications or adaptations are made.
spellingShingle Case Reports
Ledger, Thomas
Braude, Stanley
Multiple complications of advanced IPF in an individual patient presentation
title Multiple complications of advanced IPF in an individual patient presentation
title_full Multiple complications of advanced IPF in an individual patient presentation
title_fullStr Multiple complications of advanced IPF in an individual patient presentation
title_full_unstemmed Multiple complications of advanced IPF in an individual patient presentation
title_short Multiple complications of advanced IPF in an individual patient presentation
title_sort multiple complications of advanced ipf in an individual patient presentation
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10037082/
https://www.ncbi.nlm.nih.gov/pubmed/36970298
http://dx.doi.org/10.1002/rcr2.1118
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