Cargando…

A 20-Year Longitudinal Study of Plasma Chitotriosidase Activity in Treated Gaucher Disease Type 1 and 3 Patients—A Qualitative and Quantitative Approach

Chitotriosidase is an enzyme produced and secreted in large amounts by activated macrophages, especially macrophages loaded with phagocytozed glycosphingolipid in Gaucher disease. Macrophages phagocytose decayed blood cells that contain a lot of sphingolipid-rich cell membranes. In Gaucher disease,...

Descripción completa

Detalles Bibliográficos
Autores principales: Szymańska-Rożek, Paulina, Czartoryska, Barbara, Kleinotiene, Grazina, Lipiński, Patryk, Tylki-Szymańska, Anna, Ługowska, Agnieszka
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10046580/
https://www.ncbi.nlm.nih.gov/pubmed/36979371
http://dx.doi.org/10.3390/biom13030436