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A 20-Year Longitudinal Study of Plasma Chitotriosidase Activity in Treated Gaucher Disease Type 1 and 3 Patients—A Qualitative and Quantitative Approach
Chitotriosidase is an enzyme produced and secreted in large amounts by activated macrophages, especially macrophages loaded with phagocytozed glycosphingolipid in Gaucher disease. Macrophages phagocytose decayed blood cells that contain a lot of sphingolipid-rich cell membranes. In Gaucher disease,...
Autores principales: | Szymańska-Rożek, Paulina, Czartoryska, Barbara, Kleinotiene, Grazina, Lipiński, Patryk, Tylki-Szymańska, Anna, Ługowska, Agnieszka |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10046580/ https://www.ncbi.nlm.nih.gov/pubmed/36979371 http://dx.doi.org/10.3390/biom13030436 |
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