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Cystic Fibrosis Bone Disease: The Interplay between CFTR Dysfunction and Chronic Inflammation

Cystic fibrosis is a monogenic disease with a multisystemic phenotype, ranging from predisposition to chronic lung infection and inflammation to reduced bone mass. The exact mechanisms unbalancing the maintenance of an optimal bone mass in cystic fibrosis patients remain unknown. Multiple factors ma...

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Detalles Bibliográficos
Autores principales:	Fonseca, Óscar, Gomes, Maria Salomé, Amorim, Maria Adelina, Gomes, Ana Cordeiro
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	MDPI 2023
Materias:	Review
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10046889/ https://www.ncbi.nlm.nih.gov/pubmed/36979360 http://dx.doi.org/10.3390/biom13030425

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