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A rare case of partial cor triatriatum diagnosed at an adult age: a case report

BACKGROUND: Cor triatriatum sinistra (CTS) is a rare condition where the left atrium (LA) is divided by a thin membrane into an upper and lower chamber. Incidentally, the diagnosis is made in late adulthood, usually because of a favourable variant such as in our patient who presented with partial CT...

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Autores principales: von Bartheld, Bob, Rijnierse, Mischa, van Loon, Ramon, Meijboom, Lilian
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Oxford University Press 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10064265/
https://www.ncbi.nlm.nih.gov/pubmed/37006802
http://dx.doi.org/10.1093/ehjcr/ytad082
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author von Bartheld, Bob
Rijnierse, Mischa
van Loon, Ramon
Meijboom, Lilian
author_facet von Bartheld, Bob
Rijnierse, Mischa
van Loon, Ramon
Meijboom, Lilian
author_sort von Bartheld, Bob
collection PubMed
description BACKGROUND: Cor triatriatum sinistra (CTS) is a rare condition where the left atrium (LA) is divided by a thin membrane into an upper and lower chamber. Incidentally, the diagnosis is made in late adulthood, usually because of a favourable variant such as in our patient who presented with partial CTS. CASE SUMMARY: We present the case of a 62-year-old female who presented with COVID-19. She was known for longstanding symptoms of dyspnoea on exertion as well as a minor stroke several years ago. Computed tomography on admission suggested there was a mass in the LA but transthoracic echocardiography and cardiac magnetic resonance imaging revealed the diagnosis of partial CTS in which the superior compartment received pulmonary venous drainage from the right lung and the left-sided pulmonary veins drained into the inferior chamber. Since there were signs of chronic pulmonary oedema she successfully underwent balloon dilatation of the membrane resulting in remission of symptoms and normalization of the pressure in the accessory chamber. DISCUSSION: Partial CTS is a rare variant of CTS. Since part of the pulmonary veins drains in the lower chamber of the LA (and thereby unload the right ventricle), it is a favourable variant and patients may present later in life when membrane orifices calcify or it may be discovered as an incidental finding. In some patients requiring intervention, balloon dilatation of the membrane may be considered as an alternative to surgical removal of the membrane by thoracotomy.
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spelling pubmed-100642652023-04-01 A rare case of partial cor triatriatum diagnosed at an adult age: a case report von Bartheld, Bob Rijnierse, Mischa van Loon, Ramon Meijboom, Lilian Eur Heart J Case Rep Case Report BACKGROUND: Cor triatriatum sinistra (CTS) is a rare condition where the left atrium (LA) is divided by a thin membrane into an upper and lower chamber. Incidentally, the diagnosis is made in late adulthood, usually because of a favourable variant such as in our patient who presented with partial CTS. CASE SUMMARY: We present the case of a 62-year-old female who presented with COVID-19. She was known for longstanding symptoms of dyspnoea on exertion as well as a minor stroke several years ago. Computed tomography on admission suggested there was a mass in the LA but transthoracic echocardiography and cardiac magnetic resonance imaging revealed the diagnosis of partial CTS in which the superior compartment received pulmonary venous drainage from the right lung and the left-sided pulmonary veins drained into the inferior chamber. Since there were signs of chronic pulmonary oedema she successfully underwent balloon dilatation of the membrane resulting in remission of symptoms and normalization of the pressure in the accessory chamber. DISCUSSION: Partial CTS is a rare variant of CTS. Since part of the pulmonary veins drains in the lower chamber of the LA (and thereby unload the right ventricle), it is a favourable variant and patients may present later in life when membrane orifices calcify or it may be discovered as an incidental finding. In some patients requiring intervention, balloon dilatation of the membrane may be considered as an alternative to surgical removal of the membrane by thoracotomy. Oxford University Press 2023-02-13 /pmc/articles/PMC10064265/ /pubmed/37006802 http://dx.doi.org/10.1093/ehjcr/ytad082 Text en © The Author(s) 2023. Published by Oxford University Press on behalf of the European Society of Cardiology. https://creativecommons.org/licenses/by-nc/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial License (https://creativecommons.org/licenses/by-nc/4.0/), which permits non-commercial re-use, distribution, and reproduction in any medium, provided the original work is properly cited. For commercial re-use, please contact journals.permissions@oup.com
spellingShingle Case Report
von Bartheld, Bob
Rijnierse, Mischa
van Loon, Ramon
Meijboom, Lilian
A rare case of partial cor triatriatum diagnosed at an adult age: a case report
title A rare case of partial cor triatriatum diagnosed at an adult age: a case report
title_full A rare case of partial cor triatriatum diagnosed at an adult age: a case report
title_fullStr A rare case of partial cor triatriatum diagnosed at an adult age: a case report
title_full_unstemmed A rare case of partial cor triatriatum diagnosed at an adult age: a case report
title_short A rare case of partial cor triatriatum diagnosed at an adult age: a case report
title_sort rare case of partial cor triatriatum diagnosed at an adult age: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10064265/
https://www.ncbi.nlm.nih.gov/pubmed/37006802
http://dx.doi.org/10.1093/ehjcr/ytad082
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