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A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia

Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, pat...

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Autores principales: Dronamraju, Veena, McSurdy, Kaitlyn, Graham, Ryan, Rali, Parth, Kumaran, Maruti, Proca, Daniela, Lashari, Bilal, Toyoda, Yoshiya, Gupta, Rohit
Formato: Online Artículo Texto
Lenguaje:English
Publicado: John Wiley and Sons Inc. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10064855/
https://www.ncbi.nlm.nih.gov/pubmed/37007934
http://dx.doi.org/10.1002/pul2.12214
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author Dronamraju, Veena
McSurdy, Kaitlyn
Graham, Ryan
Rali, Parth
Kumaran, Maruti
Proca, Daniela
Lashari, Bilal
Toyoda, Yoshiya
Gupta, Rohit
author_facet Dronamraju, Veena
McSurdy, Kaitlyn
Graham, Ryan
Rali, Parth
Kumaran, Maruti
Proca, Daniela
Lashari, Bilal
Toyoda, Yoshiya
Gupta, Rohit
author_sort Dronamraju, Veena
collection PubMed
description Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID‐19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately.
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spelling pubmed-100648552023-04-01 A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia Dronamraju, Veena McSurdy, Kaitlyn Graham, Ryan Rali, Parth Kumaran, Maruti Proca, Daniela Lashari, Bilal Toyoda, Yoshiya Gupta, Rohit Pulm Circ Case Reports Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID‐19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately. John Wiley and Sons Inc. 2023-03-31 /pmc/articles/PMC10064855/ /pubmed/37007934 http://dx.doi.org/10.1002/pul2.12214 Text en © 2023 The Authors. Pulmonary Circulation published by John Wiley & Sons Ltd on behalf of Pulmonary Vascular Research Institute. https://creativecommons.org/licenses/by-nc/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc/4.0/ (https://creativecommons.org/licenses/by-nc/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited and is not used for commercial purposes.
spellingShingle Case Reports
Dronamraju, Veena
McSurdy, Kaitlyn
Graham, Ryan
Rali, Parth
Kumaran, Maruti
Proca, Daniela
Lashari, Bilal
Toyoda, Yoshiya
Gupta, Rohit
A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
title A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
title_full A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
title_fullStr A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
title_full_unstemmed A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
title_short A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
title_sort rare case of rosai–dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10064855/
https://www.ncbi.nlm.nih.gov/pubmed/37007934
http://dx.doi.org/10.1002/pul2.12214
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