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A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia
Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, pat...
Autores principales: | , , , , , , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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John Wiley and Sons Inc.
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10064855/ https://www.ncbi.nlm.nih.gov/pubmed/37007934 http://dx.doi.org/10.1002/pul2.12214 |
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author | Dronamraju, Veena McSurdy, Kaitlyn Graham, Ryan Rali, Parth Kumaran, Maruti Proca, Daniela Lashari, Bilal Toyoda, Yoshiya Gupta, Rohit |
author_facet | Dronamraju, Veena McSurdy, Kaitlyn Graham, Ryan Rali, Parth Kumaran, Maruti Proca, Daniela Lashari, Bilal Toyoda, Yoshiya Gupta, Rohit |
author_sort | Dronamraju, Veena |
collection | PubMed |
description | Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID‐19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately. |
format | Online Article Text |
id | pubmed-10064855 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | John Wiley and Sons Inc. |
record_format | MEDLINE/PubMed |
spelling | pubmed-100648552023-04-01 A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia Dronamraju, Veena McSurdy, Kaitlyn Graham, Ryan Rali, Parth Kumaran, Maruti Proca, Daniela Lashari, Bilal Toyoda, Yoshiya Gupta, Rohit Pulm Circ Case Reports Rosai–Dorfman disease (RDD) is a rare form of non‐Langerhans histiocytosis. It is often idiopathic in etiology, but has been associated with viral, autoimmune, and malignant disease. Adequate diagnosis of RDD requires a combination of clinical symptoms, radiography, and histology. Most commonly, patients with RDD present with cervical lymphadenopathy. We describe a case of a young female who was initially thought to have a pulmonary embolism at the time of a COVID‐19 infection but was noted to have a rare occurrence of RDD presenting as a pulmonary artery mass upon further evaluation of radiology and histology. Though RDD is frequently benign, extranodal involvement can progress to end organ damage and must be recognized appropriately. John Wiley and Sons Inc. 2023-03-31 /pmc/articles/PMC10064855/ /pubmed/37007934 http://dx.doi.org/10.1002/pul2.12214 Text en © 2023 The Authors. Pulmonary Circulation published by John Wiley & Sons Ltd on behalf of Pulmonary Vascular Research Institute. https://creativecommons.org/licenses/by-nc/4.0/This is an open access article under the terms of the http://creativecommons.org/licenses/by-nc/4.0/ (https://creativecommons.org/licenses/by-nc/4.0/) License, which permits use, distribution and reproduction in any medium, provided the original work is properly cited and is not used for commercial purposes. |
spellingShingle | Case Reports Dronamraju, Veena McSurdy, Kaitlyn Graham, Ryan Rali, Parth Kumaran, Maruti Proca, Daniela Lashari, Bilal Toyoda, Yoshiya Gupta, Rohit A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
title | A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
title_full | A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
title_fullStr | A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
title_full_unstemmed | A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
title_short | A rare case of Rosai–Dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
title_sort | rare case of rosai–dorfman disease presenting as a pulmonary artery mass in a 33‐year‐old female with hypoxia |
topic | Case Reports |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10064855/ https://www.ncbi.nlm.nih.gov/pubmed/37007934 http://dx.doi.org/10.1002/pul2.12214 |
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