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Nerve pathology is prevented by linker proteins in mouse models for LAMA2-related muscular dystrophy

LAMA2-related muscular dystrophy (LAMA2 MD or MDC1A) is a devastating congenital muscular dystrophy that is caused by mutations in the LAMA2 gene encoding laminin-α2, the long chain of several heterotrimeric laminins. Laminins are essential components of the extracellular matrix that interface with...

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Detalles Bibliográficos
Autores principales:	Reinhard, Judith R, Porrello, Emanuela, Lin, Shuo, Pelczar, Pawel, Previtali, Stefano C, Rüegg, Markus A
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Oxford University Press 2023
Materias:	Biological, Health, and Medical Sciences
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10082391/ https://www.ncbi.nlm.nih.gov/pubmed/37038437 http://dx.doi.org/10.1093/pnasnexus/pgad083

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