A Rare Case of Suspected Neuronal Intranuclear Inclusion Disease Requiring Differentiation From Neuro-Behçet’s Disease

A 69-year-old male patient with a long-standing history of Behçet’s disease was admitted to another hospital with minor physical injuries after a traffic accident. However, the patient was subsequently transferred to our facility because of a prolonged disorder of consciousness suspected to be related to neuro-Behçet’s disease (NBD). A thorough patient evaluation for determining the most appropriate treatment course led to a strong suspicion of neuronal intranuclear inclusion disease and predominantly ruled out NBD. This eliminated the need for unnecessary immunosuppressive intervention. Thereafter, the patient was transferred to a long-term care facility. This case highlights the importance of careful identification of pathological conditions before developing a treatment plan, regardless of the presence or absence of an underlying disease.