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A rare metastatic mesenteric malignant PEComa with TSC2 mutation treated with palliative surgical resection and nab-sirolimus: a case report

BACKGROUND: Malignant perivascular epithelioid cell tumors (PEComas) are exceedingly rare malignant mesenchymal neoplasms with characteristic morphological and immunohistochemical (IHC) patterns. However, some malignant PEComas are poorly differentiated with atypical histopathological features, maki...

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Detalles Bibliográficos
Autores principales:	Meredith, Luke, Chao, Timothy, Nevler, Avinoam, Basu Mallick, Atrayee, Singla, Rajan K., McCue, Peter A., Bowne, Wilbur B., Jiang, Wei
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2023
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10088294/ https://www.ncbi.nlm.nih.gov/pubmed/37041531 http://dx.doi.org/10.1186/s13000-023-01323-x

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