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Short Telomere Syndrome presenting with pulmonary fibrosis, liver cirrhosis and hepatopulmonary syndrome: a case report

BACKGROUND: Idiopathic pulmonary fibrosis is thought to result from aberrant post-injury activation of epithelial cells leading to fibroblast proliferation and activation. A number of genetic aetiologies have been implicated in this disease process, including, among others, the short telomere syndro...

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Detalles Bibliográficos
Autores principales:	Baird, Andrew, Gomes, Marcio, Souza, Carolina A., Magner, Kate, Alvarez, Gonzalo
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	BioMed Central 2023
Materias:	Case Report
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10091635/ https://www.ncbi.nlm.nih.gov/pubmed/37041499 http://dx.doi.org/10.1186/s12890-023-02378-8

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