Middle ear cholesteatoma resection under general anesthesia in patients with congenital methemoglobinemia: A case report

Congenital methemoglobinemia is a rare cyanosis cause that can be manifested in affected individuals. We report a case of congenital methemoglobinemia after middle ear cholesteatoma resection under general anesthesia. PATIENT CONCERNS: The primary concern of the patient is to safely perform cholesteatoma resection of the middle ear to reduce the pain associated with years of surgery and to survive the perioperative period. DIAGNOSES: Congenital methemoglobinemia type 1. INTERVENTIONS: The patient underwent general anesthesia and cholesteatoma resection of the middle ear. OUTCOMES: The patient successfully underwent cholesteatoma resection in the middle ear under general anesthesia and went through the perioperative period smoothly, and successfully returned to society. LESSONS: For patients requiring general anesthesia complicated with rare methemoglobinemia, we improve the awareness of crisis and make comprehensive preparation and monitoring, learn the pathophysiological mechanism related to the disease, so as to protect the operation of methemoglobin patients under general anesthesia.