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Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
An uncommon benign mixed mesenchymal tumor called extrarenal retroperitoneal angiomyolipoma (ERAML) comprises thick-walled blood vessels, smooth muscle cells, and mature fat cells. Angiomyolipoma often develops in the kidneys, with extrarenal locations being uncommon. Many angiomyolipomas are uninte...
Autores principales: | , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
Cureus
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10112489/ https://www.ncbi.nlm.nih.gov/pubmed/37082478 http://dx.doi.org/10.7759/cureus.36357 |
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author | Thakur, Bharati Hiwale, K. M. |
author_facet | Thakur, Bharati Hiwale, K. M. |
author_sort | Thakur, Bharati |
collection | PubMed |
description | An uncommon benign mixed mesenchymal tumor called extrarenal retroperitoneal angiomyolipoma (ERAML) comprises thick-walled blood vessels, smooth muscle cells, and mature fat cells. Angiomyolipoma often develops in the kidneys, with extrarenal locations being uncommon. Many angiomyolipomas are unintentionally discovered when a person undergoes other medical issues. A 35-year-old man presented with a history of difficulty breathing and was on antibiotics. On follow-up, CT revealed a 22.5 × 14.3 × 8.6 cm right retroperitoneal mass. The retroperitoneal mass was resected en bloc at laparotomy and sent for histopathological examination. The grossly resected specimen was a smooth, well-circumscribed, yellowish-red retroperitoneal mass measuring 23 × 15 × 9 cm. The microscopic section reveals a tumor with prominent blood vessels and fatty tissue composed of spindle cells arranged into fascicles. The final diagnosis for this case is ERAML, which was challenging to distinguish from liposarcoma. |
format | Online Article Text |
id | pubmed-10112489 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | Cureus |
record_format | MEDLINE/PubMed |
spelling | pubmed-101124892023-04-19 Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case Thakur, Bharati Hiwale, K. M. Cureus Pathology An uncommon benign mixed mesenchymal tumor called extrarenal retroperitoneal angiomyolipoma (ERAML) comprises thick-walled blood vessels, smooth muscle cells, and mature fat cells. Angiomyolipoma often develops in the kidneys, with extrarenal locations being uncommon. Many angiomyolipomas are unintentionally discovered when a person undergoes other medical issues. A 35-year-old man presented with a history of difficulty breathing and was on antibiotics. On follow-up, CT revealed a 22.5 × 14.3 × 8.6 cm right retroperitoneal mass. The retroperitoneal mass was resected en bloc at laparotomy and sent for histopathological examination. The grossly resected specimen was a smooth, well-circumscribed, yellowish-red retroperitoneal mass measuring 23 × 15 × 9 cm. The microscopic section reveals a tumor with prominent blood vessels and fatty tissue composed of spindle cells arranged into fascicles. The final diagnosis for this case is ERAML, which was challenging to distinguish from liposarcoma. Cureus 2023-03-19 /pmc/articles/PMC10112489/ /pubmed/37082478 http://dx.doi.org/10.7759/cureus.36357 Text en Copyright © 2023, Thakur et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited. |
spellingShingle | Pathology Thakur, Bharati Hiwale, K. M. Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case |
title | Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case |
title_full | Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case |
title_fullStr | Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case |
title_full_unstemmed | Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case |
title_short | Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case |
title_sort | intricacy in the diagnosis of retroperitoneal angiomyolipoma: a rare case |
topic | Pathology |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10112489/ https://www.ncbi.nlm.nih.gov/pubmed/37082478 http://dx.doi.org/10.7759/cureus.36357 |
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