Cargando…

Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case

An uncommon benign mixed mesenchymal tumor called extrarenal retroperitoneal angiomyolipoma (ERAML) comprises thick-walled blood vessels, smooth muscle cells, and mature fat cells. Angiomyolipoma often develops in the kidneys, with extrarenal locations being uncommon. Many angiomyolipomas are uninte...

Descripción completa

Detalles Bibliográficos
Autores principales: Thakur, Bharati, Hiwale, K. M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10112489/
https://www.ncbi.nlm.nih.gov/pubmed/37082478
http://dx.doi.org/10.7759/cureus.36357
_version_ 1785027633321345024
author Thakur, Bharati
Hiwale, K. M.
author_facet Thakur, Bharati
Hiwale, K. M.
author_sort Thakur, Bharati
collection PubMed
description An uncommon benign mixed mesenchymal tumor called extrarenal retroperitoneal angiomyolipoma (ERAML) comprises thick-walled blood vessels, smooth muscle cells, and mature fat cells. Angiomyolipoma often develops in the kidneys, with extrarenal locations being uncommon. Many angiomyolipomas are unintentionally discovered when a person undergoes other medical issues. A 35-year-old man presented with a history of difficulty breathing and was on antibiotics. On follow-up, CT revealed a 22.5 × 14.3 × 8.6 cm right retroperitoneal mass. The retroperitoneal mass was resected en bloc at laparotomy and sent for histopathological examination. The grossly resected specimen was a smooth, well-circumscribed, yellowish-red retroperitoneal mass measuring 23 × 15 × 9 cm. The microscopic section reveals a tumor with prominent blood vessels and fatty tissue composed of spindle cells arranged into fascicles. The final diagnosis for this case is ERAML, which was challenging to distinguish from liposarcoma.
format Online
Article
Text
id pubmed-10112489
institution National Center for Biotechnology Information
language English
publishDate 2023
publisher Cureus
record_format MEDLINE/PubMed
spelling pubmed-101124892023-04-19 Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case Thakur, Bharati Hiwale, K. M. Cureus Pathology An uncommon benign mixed mesenchymal tumor called extrarenal retroperitoneal angiomyolipoma (ERAML) comprises thick-walled blood vessels, smooth muscle cells, and mature fat cells. Angiomyolipoma often develops in the kidneys, with extrarenal locations being uncommon. Many angiomyolipomas are unintentionally discovered when a person undergoes other medical issues. A 35-year-old man presented with a history of difficulty breathing and was on antibiotics. On follow-up, CT revealed a 22.5 × 14.3 × 8.6 cm right retroperitoneal mass. The retroperitoneal mass was resected en bloc at laparotomy and sent for histopathological examination. The grossly resected specimen was a smooth, well-circumscribed, yellowish-red retroperitoneal mass measuring 23 × 15 × 9 cm. The microscopic section reveals a tumor with prominent blood vessels and fatty tissue composed of spindle cells arranged into fascicles. The final diagnosis for this case is ERAML, which was challenging to distinguish from liposarcoma. Cureus 2023-03-19 /pmc/articles/PMC10112489/ /pubmed/37082478 http://dx.doi.org/10.7759/cureus.36357 Text en Copyright © 2023, Thakur et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Pathology
Thakur, Bharati
Hiwale, K. M.
Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
title Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
title_full Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
title_fullStr Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
title_full_unstemmed Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
title_short Intricacy in the Diagnosis of Retroperitoneal Angiomyolipoma: A Rare Case
title_sort intricacy in the diagnosis of retroperitoneal angiomyolipoma: a rare case
topic Pathology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10112489/
https://www.ncbi.nlm.nih.gov/pubmed/37082478
http://dx.doi.org/10.7759/cureus.36357
work_keys_str_mv AT thakurbharati intricacyinthediagnosisofretroperitonealangiomyolipomaararecase
AT hiwalekm intricacyinthediagnosisofretroperitonealangiomyolipomaararecase