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Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population

Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare fulminant variant of pityriasis lichenoides et varioliformis acuta (PLEVA) that is characterized by a large ulceronecrotic appearance with high fever and a variety of systemic symptoms. We report here a case of FUMHD in a 17-year-old m...

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Detalles Bibliográficos
Autores principales: LIU, Jue, ZHONG, Jianbo, WANG, Qiaowei, CAI, Yinglian, CHEN, Jian
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Medical Journals Sweden, on behalf of the Society for Publication of Acta Dermato-Venereologica 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10128150/
https://www.ncbi.nlm.nih.gov/pubmed/37073962
http://dx.doi.org/10.2340/actadv.v103.4806
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author LIU, Jue
ZHONG, Jianbo
WANG, Qiaowei
CAI, Yinglian
CHEN, Jian
author_facet LIU, Jue
ZHONG, Jianbo
WANG, Qiaowei
CAI, Yinglian
CHEN, Jian
author_sort LIU, Jue
collection PubMed
description Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare fulminant variant of pityriasis lichenoides et varioliformis acuta (PLEVA) that is characterized by a large ulceronecrotic appearance with high fever and a variety of systemic symptoms. We report here a case of FUMHD in a 17-year-old male Chinese patient who was treated successfully with a combination therapy of methotrexate, methylprednisolone, and intravenous immunoglobulin. In addition, a literature review was conducted to summarize the key characteristics of paediatric FUMHD cases.
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spelling pubmed-101281502023-04-26 Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population LIU, Jue ZHONG, Jianbo WANG, Qiaowei CAI, Yinglian CHEN, Jian Acta Derm Venereol Review Article Febrile ulceronecrotic Mucha-Habermann disease (FUMHD) is a rare fulminant variant of pityriasis lichenoides et varioliformis acuta (PLEVA) that is characterized by a large ulceronecrotic appearance with high fever and a variety of systemic symptoms. We report here a case of FUMHD in a 17-year-old male Chinese patient who was treated successfully with a combination therapy of methotrexate, methylprednisolone, and intravenous immunoglobulin. In addition, a literature review was conducted to summarize the key characteristics of paediatric FUMHD cases. Medical Journals Sweden, on behalf of the Society for Publication of Acta Dermato-Venereologica 2023-04-19 /pmc/articles/PMC10128150/ /pubmed/37073962 http://dx.doi.org/10.2340/actadv.v103.4806 Text en © Published by Medical Journals Sweden, on behalf of the Foundation for Rehabilitation Information https://creativecommons.org/licenses/by-nc/4.0/This is an Open Access article distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 International License (https://creativecommons.org/licenses/by-nc/4.0/)
spellingShingle Review Article
LIU, Jue
ZHONG, Jianbo
WANG, Qiaowei
CAI, Yinglian
CHEN, Jian
Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population
title Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population
title_full Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population
title_fullStr Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population
title_full_unstemmed Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population
title_short Febrile Ulceronecrotic Mucha-Habermann Disease: A Case Report and Review of Literature in the Paediatric Population
title_sort febrile ulceronecrotic mucha-habermann disease: a case report and review of literature in the paediatric population
topic Review Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10128150/
https://www.ncbi.nlm.nih.gov/pubmed/37073962
http://dx.doi.org/10.2340/actadv.v103.4806
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