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Therapy of Patients with Cardiac Malposition
Positional abnormalities per se do not require treatment, but in their place, the accompanying pulmonary pathology in dextroposition patients and pathophysiologic hemodynamic abnormalities resulting from multiple defects in patients with cardiac malposition should be the focus of treatment. At the t...
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Formato: | Online Artículo Texto |
Lenguaje: | English |
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MDPI
2023
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Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10137016/ https://www.ncbi.nlm.nih.gov/pubmed/37189988 http://dx.doi.org/10.3390/children10040739 |
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author | Rao, P. Syamasundar |
author_facet | Rao, P. Syamasundar |
author_sort | Rao, P. Syamasundar |
collection | PubMed |
description | Positional abnormalities per se do not require treatment, but in their place, the accompanying pulmonary pathology in dextroposition patients and pathophysiologic hemodynamic abnormalities resulting from multiple defects in patients with cardiac malposition should be the focus of treatment. At the time of the first presentation, treating the pathophysiologic aberrations caused by the defect complex, whether it is by improving the pulmonary blood flow or restricting it, is the first step. Some patients with simpler or single defects are amenable to surgical or transcatheter therapy and should be treated accordingly. Other associated defects should also be treated appropriately. Biventricular or univentricular repair dependent on the patient’s cardiac structure should be planned. Complications in-between Fontan stages and after conclusion of Fontan surgery may occur and should be promptly diagnosed and addressed accordingly. Several other cardiac abnormalities unrelated to the initially identified heart defects may manifest in adulthood, and they should also be treated. |
format | Online Article Text |
id | pubmed-10137016 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-101370162023-04-28 Therapy of Patients with Cardiac Malposition Rao, P. Syamasundar Children (Basel) Review Positional abnormalities per se do not require treatment, but in their place, the accompanying pulmonary pathology in dextroposition patients and pathophysiologic hemodynamic abnormalities resulting from multiple defects in patients with cardiac malposition should be the focus of treatment. At the time of the first presentation, treating the pathophysiologic aberrations caused by the defect complex, whether it is by improving the pulmonary blood flow or restricting it, is the first step. Some patients with simpler or single defects are amenable to surgical or transcatheter therapy and should be treated accordingly. Other associated defects should also be treated appropriately. Biventricular or univentricular repair dependent on the patient’s cardiac structure should be planned. Complications in-between Fontan stages and after conclusion of Fontan surgery may occur and should be promptly diagnosed and addressed accordingly. Several other cardiac abnormalities unrelated to the initially identified heart defects may manifest in adulthood, and they should also be treated. MDPI 2023-04-17 /pmc/articles/PMC10137016/ /pubmed/37189988 http://dx.doi.org/10.3390/children10040739 Text en © 2023 by the author. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Review Rao, P. Syamasundar Therapy of Patients with Cardiac Malposition |
title | Therapy of Patients with Cardiac Malposition |
title_full | Therapy of Patients with Cardiac Malposition |
title_fullStr | Therapy of Patients with Cardiac Malposition |
title_full_unstemmed | Therapy of Patients with Cardiac Malposition |
title_short | Therapy of Patients with Cardiac Malposition |
title_sort | therapy of patients with cardiac malposition |
topic | Review |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10137016/ https://www.ncbi.nlm.nih.gov/pubmed/37189988 http://dx.doi.org/10.3390/children10040739 |
work_keys_str_mv | AT raopsyamasundar therapyofpatientswithcardiacmalposition |