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Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intuba...
Autores principales: | , , , |
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Formato: | Online Artículo Texto |
Lenguaje: | English |
Publicado: |
MDPI
2023
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Materias: | |
Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10137264/ https://www.ncbi.nlm.nih.gov/pubmed/37189880 http://dx.doi.org/10.3390/children10040631 |
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author | Park, Sang Jin Baek, Jongyoon Chun, Suyoun Choi, Eun Kyung |
author_facet | Park, Sang Jin Baek, Jongyoon Chun, Suyoun Choi, Eun Kyung |
author_sort | Park, Sang Jin |
collection | PubMed |
description | Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intubation, seizure control due to lissencephaly, and any other clinical complications. Herein, we report a case of anesthetic management in a child with MDS and describe relevant clinical features in a perioperative anesthetic setting. This case highlights the importance of difficult airway manipulation using a videolaryngoscope, seizure management with regard to anesthetics use, and the low validity of BIS monitoring in patients with MDS. |
format | Online Article Text |
id | pubmed-10137264 |
institution | National Center for Biotechnology Information |
language | English |
publishDate | 2023 |
publisher | MDPI |
record_format | MEDLINE/PubMed |
spelling | pubmed-101372642023-04-28 Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report Park, Sang Jin Baek, Jongyoon Chun, Suyoun Choi, Eun Kyung Children (Basel) Case Report Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intubation, seizure control due to lissencephaly, and any other clinical complications. Herein, we report a case of anesthetic management in a child with MDS and describe relevant clinical features in a perioperative anesthetic setting. This case highlights the importance of difficult airway manipulation using a videolaryngoscope, seizure management with regard to anesthetics use, and the low validity of BIS monitoring in patients with MDS. MDPI 2023-03-28 /pmc/articles/PMC10137264/ /pubmed/37189880 http://dx.doi.org/10.3390/children10040631 Text en © 2023 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/). |
spellingShingle | Case Report Park, Sang Jin Baek, Jongyoon Chun, Suyoun Choi, Eun Kyung Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
title | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
title_full | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
title_fullStr | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
title_full_unstemmed | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
title_short | Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report |
title_sort | anesthetic management and bispectral index in a child with miller–dieker syndrome: a case report |
topic | Case Report |
url | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10137264/ https://www.ncbi.nlm.nih.gov/pubmed/37189880 http://dx.doi.org/10.3390/children10040631 |
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