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Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report

Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intuba...

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Detalles Bibliográficos
Autores principales: Park, Sang Jin, Baek, Jongyoon, Chun, Suyoun, Choi, Eun Kyung
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10137264/
https://www.ncbi.nlm.nih.gov/pubmed/37189880
http://dx.doi.org/10.3390/children10040631
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author Park, Sang Jin
Baek, Jongyoon
Chun, Suyoun
Choi, Eun Kyung
author_facet Park, Sang Jin
Baek, Jongyoon
Chun, Suyoun
Choi, Eun Kyung
author_sort Park, Sang Jin
collection PubMed
description Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intubation, seizure control due to lissencephaly, and any other clinical complications. Herein, we report a case of anesthetic management in a child with MDS and describe relevant clinical features in a perioperative anesthetic setting. This case highlights the importance of difficult airway manipulation using a videolaryngoscope, seizure management with regard to anesthetics use, and the low validity of BIS monitoring in patients with MDS.
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spelling pubmed-101372642023-04-28 Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report Park, Sang Jin Baek, Jongyoon Chun, Suyoun Choi, Eun Kyung Children (Basel) Case Report Miller–Dieker syndrome (MDS) is a genetic disorder characterized by classic lissencephaly, distinctive facial features, intellectual disability, seizures, and early death. The anesthetic management of patients with MDS should focus on airway manipulation with the risk of potentially difficult intubation, seizure control due to lissencephaly, and any other clinical complications. Herein, we report a case of anesthetic management in a child with MDS and describe relevant clinical features in a perioperative anesthetic setting. This case highlights the importance of difficult airway manipulation using a videolaryngoscope, seizure management with regard to anesthetics use, and the low validity of BIS monitoring in patients with MDS. MDPI 2023-03-28 /pmc/articles/PMC10137264/ /pubmed/37189880 http://dx.doi.org/10.3390/children10040631 Text en © 2023 by the authors. https://creativecommons.org/licenses/by/4.0/Licensee MDPI, Basel, Switzerland. This article is an open access article distributed under the terms and conditions of the Creative Commons Attribution (CC BY) license (https://creativecommons.org/licenses/by/4.0/).
spellingShingle Case Report
Park, Sang Jin
Baek, Jongyoon
Chun, Suyoun
Choi, Eun Kyung
Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
title Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
title_full Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
title_fullStr Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
title_full_unstemmed Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
title_short Anesthetic Management and Bispectral Index in a Child with Miller–Dieker Syndrome: A Case Report
title_sort anesthetic management and bispectral index in a child with miller–dieker syndrome: a case report
topic Case Report
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10137264/
https://www.ncbi.nlm.nih.gov/pubmed/37189880
http://dx.doi.org/10.3390/children10040631
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