Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report

Chiari malformation is a clinico-radiological entity defined by herniation of rhombencephalic structures through the foramen magnum. The most common type, Chiari I, involves herniation of the cerebellar tonsils specifically. We present the case of a 2-year-old with three weeks of progressive bilater...

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Autores principales: Lo, Angelina, LaRocca, Megan C., Whalen, Danielle, Gonzalez-Castillo, Zurisadai
Formato: Online Artículo Texto
Lenguaje:English
Publicado: SAGE Publications 2023
Materias:
Original Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10141243/
https://www.ncbi.nlm.nih.gov/pubmed/37122875
http://dx.doi.org/10.1177/2329048X231169510
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author Lo, Angelina
LaRocca, Megan C.
Whalen, Danielle
Gonzalez-Castillo, Zurisadai
author_facet Lo, Angelina
LaRocca, Megan C.
Whalen, Danielle
Gonzalez-Castillo, Zurisadai
author_sort Lo, Angelina
collection PubMed
description Chiari malformation is a clinico-radiological entity defined by herniation of rhombencephalic structures through the foramen magnum. The most common type, Chiari I, involves herniation of the cerebellar tonsils specifically. We present the case of a 2-year-old with three weeks of progressive bilateral leg weakness, absent reflexes, and the inability to walk. The patient was found to have Chiari I with hydrocephalus and syringomyelia. This is the youngest patient reported in the literature presenting with a clinical picture of spinal shock. Early recognition of this entity allows for proper treatment and improved outcomes.
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spelling pubmed-101412432023-04-29 Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report Lo, Angelina LaRocca, Megan C. Whalen, Danielle Gonzalez-Castillo, Zurisadai Child Neurol Open Original Research Article Chiari malformation is a clinico-radiological entity defined by herniation of rhombencephalic structures through the foramen magnum. The most common type, Chiari I, involves herniation of the cerebellar tonsils specifically. We present the case of a 2-year-old with three weeks of progressive bilateral leg weakness, absent reflexes, and the inability to walk. The patient was found to have Chiari I with hydrocephalus and syringomyelia. This is the youngest patient reported in the literature presenting with a clinical picture of spinal shock. Early recognition of this entity allows for proper treatment and improved outcomes. SAGE Publications 2023-04-26 /pmc/articles/PMC10141243/ /pubmed/37122875 http://dx.doi.org/10.1177/2329048X231169510 Text en © The Author(s) 2023 https://creativecommons.org/licenses/by-nc/4.0/This article is distributed under the terms of the Creative Commons Attribution-NonCommercial 4.0 License (https://creativecommons.org/licenses/by-nc/4.0/) which permits non-commercial use, reproduction and distribution of the work without further permission provided the original work is attributed as specified on the SAGE and Open Access page (https://us.sagepub.com/en-us/nam/open-access-at-sage).
spellingShingle Original Research Article
Lo, Angelina
LaRocca, Megan C.
Whalen, Danielle
Gonzalez-Castillo, Zurisadai
Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report
title Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report
title_full Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report
title_fullStr Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report
title_full_unstemmed Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report
title_short Progressive Flaccid Paraplegia in a Toddler due to Chiari Type I Malformation Complicated with Hydrocephalus and Syringomyelia. A Case Report
title_sort progressive flaccid paraplegia in a toddler due to chiari type i malformation complicated with hydrocephalus and syringomyelia. a case report
topic Original Research Article
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10141243/
https://www.ncbi.nlm.nih.gov/pubmed/37122875
http://dx.doi.org/10.1177/2329048X231169510
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