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A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations

Cystic mucinous neoplasms of urachal origin cover a wide spectrum of benign and malignant lesions arising from the remnants of the urachus. They display various degrees of tumor cell atypia and local invasion, with no reported cases of metastasis or recurrence after complete surgical resection. We p...

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Autores principales: Mylonakis, Adam, Karydakis, Lysandros, Davakis, Spyridon, Panagakis, Andreas, Kaniadaki, Maria, Pergaris, Alexandros, Alexandrou, Andreas, Papalampros, Alexandros, Sakarellos, Panagiotis
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Cureus 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10153764/
https://www.ncbi.nlm.nih.gov/pubmed/37143634
http://dx.doi.org/10.7759/cureus.37036
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author Mylonakis, Adam
Karydakis, Lysandros
Davakis, Spyridon
Panagakis, Andreas
Kaniadaki, Maria
Pergaris, Alexandros
Alexandrou, Andreas
Papalampros, Alexandros
Sakarellos, Panagiotis
author_facet Mylonakis, Adam
Karydakis, Lysandros
Davakis, Spyridon
Panagakis, Andreas
Kaniadaki, Maria
Pergaris, Alexandros
Alexandrou, Andreas
Papalampros, Alexandros
Sakarellos, Panagiotis
author_sort Mylonakis, Adam
collection PubMed
description Cystic mucinous neoplasms of urachal origin cover a wide spectrum of benign and malignant lesions arising from the remnants of the urachus. They display various degrees of tumor cell atypia and local invasion, with no reported cases of metastasis or recurrence after complete surgical resection. We present a 47-year-old man who referred to our Surgical Department due to an abdominal cystic mass incidentally found upon abdominal ultrasound. He underwent en block resection of the cystic mass along with partial bladder dome cystectomy. The histopathology of the resected specimen revealed a cystic mucinous epithelial tumor of low malignant potential with areas of intraepithelial carcinoma. The patient showed no evidence of disease recurrence or distant metastasis 6 months after resection and is scheduled for follow-up with serial MRI or CT scans and blood tumor markers over the next 5 years.
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spelling pubmed-101537642023-05-03 A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations Mylonakis, Adam Karydakis, Lysandros Davakis, Spyridon Panagakis, Andreas Kaniadaki, Maria Pergaris, Alexandros Alexandrou, Andreas Papalampros, Alexandros Sakarellos, Panagiotis Cureus Pathology Cystic mucinous neoplasms of urachal origin cover a wide spectrum of benign and malignant lesions arising from the remnants of the urachus. They display various degrees of tumor cell atypia and local invasion, with no reported cases of metastasis or recurrence after complete surgical resection. We present a 47-year-old man who referred to our Surgical Department due to an abdominal cystic mass incidentally found upon abdominal ultrasound. He underwent en block resection of the cystic mass along with partial bladder dome cystectomy. The histopathology of the resected specimen revealed a cystic mucinous epithelial tumor of low malignant potential with areas of intraepithelial carcinoma. The patient showed no evidence of disease recurrence or distant metastasis 6 months after resection and is scheduled for follow-up with serial MRI or CT scans and blood tumor markers over the next 5 years. Cureus 2023-04-02 /pmc/articles/PMC10153764/ /pubmed/37143634 http://dx.doi.org/10.7759/cureus.37036 Text en Copyright © 2023, Mylonakis et al. https://creativecommons.org/licenses/by/3.0/This is an open access article distributed under the terms of the Creative Commons Attribution License, which permits unrestricted use, distribution, and reproduction in any medium, provided the original author and source are credited.
spellingShingle Pathology
Mylonakis, Adam
Karydakis, Lysandros
Davakis, Spyridon
Panagakis, Andreas
Kaniadaki, Maria
Pergaris, Alexandros
Alexandrou, Andreas
Papalampros, Alexandros
Sakarellos, Panagiotis
A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations
title A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations
title_full A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations
title_fullStr A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations
title_full_unstemmed A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations
title_short A Huge Asymptomatic Urachal Mucinous Cystic Carcinoma: A Case Report With Differential Diagnosis and Surgical Considerations
title_sort huge asymptomatic urachal mucinous cystic carcinoma: a case report with differential diagnosis and surgical considerations
topic Pathology
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10153764/
https://www.ncbi.nlm.nih.gov/pubmed/37143634
http://dx.doi.org/10.7759/cureus.37036
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