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A neuron‐specific Isca1 knockout rat developments multiple mitochondrial dysfunction syndromes

BACKGROUND: Multiple mitochondrial dysfunction syndromes (MMDS) are rare mitochondrial diseases caused by mutation of mitochondrial iron–sulfur cluster synthesis proteins. This study established a rat model simulating MMDS5 disease in the nervous system to investigate its pathological features and n...

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Detalles Bibliográficos
Autores principales:	Sheng, Hanxuan, Lu, Dan, Qi, Xiaolong, Ling, Yahao, Li, Jing, Zhang, Xu, Dong, Wei, Chen, Wei, Gao, Shan, Gao, Xiang, Zhang, Li, Zhang, Lianfeng
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	John Wiley and Sons Inc. 2023
Materias:	Regular Articles
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10158949/ https://www.ncbi.nlm.nih.gov/pubmed/37140997 http://dx.doi.org/10.1002/ame2.12318

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