Extracellular matrix and vascular dynamics in the kidney of a murine model for Marfan syndrome

Fibrillin-1 is a pivotal structural component of the kidney’s glomerulus and peritubular tissue. Mutations in the fibrillin-1 gene result in Marfan syndrome (MFS), an autosomal dominant disease of the connective tissue. Although the kidney is not considered a classically affected organ in MFS, sever...

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Detalles Bibliográficos
Autores principales: de Souza, Rodrigo Barbosa, Lemes, Renan Barbosa, Foresto-Neto, Orestes, Cassiano, Luara Lucena, Reinhardt, Dieter P., Meek, Keith M., Koh, Ivan Hong Jun, Lewis, Philip N., Pereira, Lygia V.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Public Library of Science 2023
Materias:
Research Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10168582/
https://www.ncbi.nlm.nih.gov/pubmed/37159453
http://dx.doi.org/10.1371/journal.pone.0285418

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