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Maintenance of chronicity signatures in fibroblasts isolated from recessive dystrophic epidermolysis bullosa chronic wound dressings under culture conditions

BACKGROUND: Recessive Dystrophic Epidermolysis Bullosa (RDEB) is a rare inherited skin disease caused by variants in the COL7A1 gene, coding for type VII collagen (C7), an important component of anchoring fibrils in the basement membrane of the epidermis. RDEB patients suffer from skin fragility sta...

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Detalles Bibliográficos
Autores principales: De Gregorio, Cristian, Catalán, Evelyng, Garrido, Gabriel, Morandé, Pilar, Bennett, Jimena Castillo, Muñoz, Catalina, Cofré, Glenda, Huang, Ya-Lin, Cuadra, Bárbara, Murgas, Paola, Calvo, Margarita, Altermatt, Fernando, Yubero, María Joao, Palisson, Francis, South, Andrew P., Ezquer, Marcelo, Fuentes, Ignacia
Formato: Online Artículo Texto
Lenguaje:English
Publicado: BioMed Central 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10170710/
https://www.ncbi.nlm.nih.gov/pubmed/37161592
http://dx.doi.org/10.1186/s40659-023-00437-2

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