Role of Partial Splenectomy in Gaucher's Disease in Resource Challenged Nations

CONTEXT: Gaucher's disease (GD) is a rare inherited metabolic disorder caused by the defective activity of glucocerebrosidase. Enzyme replacement therapy (ERT) and substrate reduction therapy are the treatment of choice. Total splenectomy has a role when the child develops complications of mass...

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Detalles Bibliográficos
Autores principales: Santanakrishnan, Ramesh, Dasaratha, Vinupriya, Munianjanappa, Narendra Babu, Javaregowda, Deepak, Saroja, Murali Govindappa
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Wolters Kluwer - Medknow 2023
Materias:
Original Article
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10185042/
https://www.ncbi.nlm.nih.gov/pubmed/37197236
http://dx.doi.org/10.4103/jiaps.jiaps_132_22

Internet

https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10185042/
https://www.ncbi.nlm.nih.gov/pubmed/37197236
http://dx.doi.org/10.4103/jiaps.jiaps_132_22

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