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Role of Partial Splenectomy in Gaucher's Disease in Resource Challenged Nations

CONTEXT: Gaucher's disease (GD) is a rare inherited metabolic disorder caused by the defective activity of glucocerebrosidase. Enzyme replacement therapy (ERT) and substrate reduction therapy are the treatment of choice. Total splenectomy has a role when the child develops complications of mass...

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Detalles Bibliográficos
Autores principales:	Santanakrishnan, Ramesh, Dasaratha, Vinupriya, Munianjanappa, Narendra Babu, Javaregowda, Deepak, Saroja, Murali Govindappa
Formato:	Online Artículo Texto
Lenguaje:	English
Publicado:	Wolters Kluwer - Medknow 2023
Materias:	Original Article
Acceso en línea:	https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10185042/ https://www.ncbi.nlm.nih.gov/pubmed/37197236 http://dx.doi.org/10.4103/jiaps.jiaps_132_22

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