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Paratesticular rhabdomyosarcoma: a rare case report from Syria

Paratesticular rhabdomyosarcoma (RMS) is a rare aggressive tumor manifesting in children and young adults. This tumor derives from mesenchymal elements of the Tunica vaginalis, epididymis, and spermatic cord. It is a very metastatic lesion that can spread by lymphatics to the iliac, para-aortic node...

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Autores principales: Sabbagh, Aziz, Hamza, Amr, Sukkari, Mohamad Walid, Fattal, Abdualh, Chammout, Anwar, Ayoub, Kusay, AL-Hadid, Ibrahim
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Lippincott Williams & Wilkins 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10205304/
https://www.ncbi.nlm.nih.gov/pubmed/37228919
http://dx.doi.org/10.1097/MS9.0000000000000461
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author Sabbagh, Aziz
Hamza, Amr
Sukkari, Mohamad Walid
Fattal, Abdualh
Chammout, Anwar
Ayoub, Kusay
AL-Hadid, Ibrahim
author_facet Sabbagh, Aziz
Hamza, Amr
Sukkari, Mohamad Walid
Fattal, Abdualh
Chammout, Anwar
Ayoub, Kusay
AL-Hadid, Ibrahim
author_sort Sabbagh, Aziz
collection PubMed
description Paratesticular rhabdomyosarcoma (RMS) is a rare aggressive tumor manifesting in children and young adults. This tumor derives from mesenchymal elements of the Tunica vaginalis, epididymis, and spermatic cord. It is a very metastatic lesion that can spread by lymphatics to the iliac, para-aortic nodes, lung, and bone. CASE PRESENTATION: In this paper, the authors report a case of a 6-year-old child who presented to the clinic with a painless mass in the right side of the scrotum. The mass was misdiagnosed and had evolved rapidly over 2 weeks. The mass measured 16×32 mm on ultrasound, and therefore, an orchiectomy was performed. The histological examination of the excised tissue confirmed the diagnosis of paratesticular RMS. DISCUSSION: Paratesticular RMS mainly presented as a painless mass in the scrotum. It was a very metastatic lesion that required an immediate management. However, a lot of cases of paratesticular RMS misdiagnosed at first time, which worsens the overall prognosis. CONCLUSION: Eventually, paratesticular RMS should be always taken into consideration when a scrotal mass is suspected. Due to its extremely serious metastatic potential, this condition requires early diagnosis and management. The treatment is currently well codified combining surgery, chemotherapy, and radiotherapy.
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spelling pubmed-102053042023-05-24 Paratesticular rhabdomyosarcoma: a rare case report from Syria Sabbagh, Aziz Hamza, Amr Sukkari, Mohamad Walid Fattal, Abdualh Chammout, Anwar Ayoub, Kusay AL-Hadid, Ibrahim Ann Med Surg (Lond) Case Reports Paratesticular rhabdomyosarcoma (RMS) is a rare aggressive tumor manifesting in children and young adults. This tumor derives from mesenchymal elements of the Tunica vaginalis, epididymis, and spermatic cord. It is a very metastatic lesion that can spread by lymphatics to the iliac, para-aortic nodes, lung, and bone. CASE PRESENTATION: In this paper, the authors report a case of a 6-year-old child who presented to the clinic with a painless mass in the right side of the scrotum. The mass was misdiagnosed and had evolved rapidly over 2 weeks. The mass measured 16×32 mm on ultrasound, and therefore, an orchiectomy was performed. The histological examination of the excised tissue confirmed the diagnosis of paratesticular RMS. DISCUSSION: Paratesticular RMS mainly presented as a painless mass in the scrotum. It was a very metastatic lesion that required an immediate management. However, a lot of cases of paratesticular RMS misdiagnosed at first time, which worsens the overall prognosis. CONCLUSION: Eventually, paratesticular RMS should be always taken into consideration when a scrotal mass is suspected. Due to its extremely serious metastatic potential, this condition requires early diagnosis and management. The treatment is currently well codified combining surgery, chemotherapy, and radiotherapy. Lippincott Williams & Wilkins 2023-04-03 /pmc/articles/PMC10205304/ /pubmed/37228919 http://dx.doi.org/10.1097/MS9.0000000000000461 Text en Copyright © 2023 the Author(s). Published by Wolters Kluwer Health, Inc. https://creativecommons.org/licenses/by-nc-nd/4.0/This is an open access article distributed under the terms of the Creative Commons Attribution-Non Commercial-No Derivatives License 4.0 (https://creativecommons.org/licenses/by-nc-nd/4.0/) (CCBY-NC-ND), where it is permissible to download and share the work provided it is properly cited. The work cannot be changed in any way or used commercially without permission from the journal. http://creativecommons.org/licenses/by-nc-nd/4.0/ (https://creativecommons.org/licenses/by-nc-nd/4.0/)
spellingShingle Case Reports
Sabbagh, Aziz
Hamza, Amr
Sukkari, Mohamad Walid
Fattal, Abdualh
Chammout, Anwar
Ayoub, Kusay
AL-Hadid, Ibrahim
Paratesticular rhabdomyosarcoma: a rare case report from Syria
title Paratesticular rhabdomyosarcoma: a rare case report from Syria
title_full Paratesticular rhabdomyosarcoma: a rare case report from Syria
title_fullStr Paratesticular rhabdomyosarcoma: a rare case report from Syria
title_full_unstemmed Paratesticular rhabdomyosarcoma: a rare case report from Syria
title_short Paratesticular rhabdomyosarcoma: a rare case report from Syria
title_sort paratesticular rhabdomyosarcoma: a rare case report from syria
topic Case Reports
url https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10205304/
https://www.ncbi.nlm.nih.gov/pubmed/37228919
http://dx.doi.org/10.1097/MS9.0000000000000461
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