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A patient with pleuroparenchymal fibroelastosis carrying a novel fibrillin-2 gene variant
Pleuroparenchymal fibroelastosis is a recently recognized clinical entity characterized by interstitial pneumonia with proliferating elastin in the upper lung regions. Pleuroparenchymal fibroelastosis is categorized as idiopathic or reported depending on the coexistent initiating factors; however, c...
| Autores principales: | , , , , , , , |
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| Formato: | Online Artículo Texto |
| Lenguaje: | English |
| Publicado: |
Elsevier
2023
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| Materias: | |
| Acceso en línea: | https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10209443/ https://www.ncbi.nlm.nih.gov/pubmed/37251355 http://dx.doi.org/10.1016/j.rmcr.2023.101870 |