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Celiac crisis as the life-threatening onset of celiac disease in children: a case report

Celiac disease (CD) is an immune-mediated enteropathy caused by a permanent sensitivity to gluten in genetically susceptible individuals. In rare cases, CD may occur with a severe potential life-threatening manifestation known as a celiac crisis (CC). This may be a consequence of a delayed diagnosis...

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Detalles Bibliográficos
Autores principales: Mauro, Angela, Casini, Francesca, Talenti, Antonella, Di Mari, Clelia, Benincaso, Anna Rita, Di Nardo, Giovanni, Bernardo, Luca
Formato: Online Artículo Texto
Lenguaje:English
Publicado: Frontiers Media S.A. 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10213434/
https://www.ncbi.nlm.nih.gov/pubmed/37252043
http://dx.doi.org/10.3389/fped.2023.1163765
Descripción
Sumario:Celiac disease (CD) is an immune-mediated enteropathy caused by a permanent sensitivity to gluten in genetically susceptible individuals. In rare cases, CD may occur with a severe potential life-threatening manifestation known as a celiac crisis (CC). This may be a consequence of a delayed diagnosis and expose patients to possible fatal complications. We report the case of a 22-month-old child admitted to our hospital for a CC characterized by weight loss, vomiting, and diarrhea associated with a malnutrition state. Early identification of symptoms of CC is essential to provide a prompt diagnosis and management.