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Accumulation of Dystrophin-Positive Muscle Fibers and Improvement of Neuromuscular Junctions in mdx Mouse Muscles after Bone Marrow Transplantation under Different Conditions

Duchenne muscular dystrophy (DMD) is a severe muscular disorder caused by mutations in the dystrophin gene. It leads to respiratory and cardiac failure and premature death at a young age. Although recent studies have greatly deepened the understanding of the primary and secondary pathogenetic mechan...

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Detalles Bibliográficos
Autores principales: Sokolova, Anastasiia V., Domnina, Alisa P., Mikhailov, Viacheslav M.
Formato: Online Artículo Texto
Lenguaje:English
Publicado: MDPI 2023
Materias:
Acceso en línea:https://www.ncbi.nlm.nih.gov/pmc/articles/PMC10219484/
https://www.ncbi.nlm.nih.gov/pubmed/37240237
http://dx.doi.org/10.3390/ijms24108892

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