A case of ganglioneuromatosis in a child and its outcome

INTRODUCTION: Ganglioneuromas (GNs) are hamartomatous tumors that originate in sympathetic ganglia and adrenal glands. Rarely, they might originate in enteric nervous system affecting its motility. Clinically they present with varying symptoms of pain abdomen, constipation and bleeding. Nevertheless, patients can remain asymptomatic for many years. CASE PRESENTATION: Author is reporting here a case of ganglioneuromatosis of intestine in a child and its effective management by a simple surgical procedure, yielding good result without morbidity. CLINICAL DISCUSSION: Intestinal ganglioneuromatosis is a rare form of benign neurogenic tumor characterized by hyperplasia of ganglion cell nerve fibers and supporting cells. CONCLUSION: Intestinal ganglioneuromatosis, diagnosed only after histopathological examination, should be managed either by conservative or surgical procedure, depending upon the clinical scenario by attending paediatric surgeon.